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Crouzon syndrome: Virtual planning of surgical treatment by application of internal distractors

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ABSTRACT

Crouzon syndrome is one of the frequent pathologies within craniosynostosis syndrome. Current progress in computers and biotechnologies allows improving surgical approach and forecasting final result of reconstruction as well. We present a case of successful surgical treatment of Crouzon syndrome, done by application of virtual planning allowing determining “monobloc” features, type of reconstruction and distraction protocol as well. A 20-year-old female had presented with craniofacial deformity. Clinical and radiological investigation revealed Crouzon syndrome. The “monobloc” creation, cranioplasty and internal distractors positioning, direction and schedule of advancement were done according to preoperative virtual planning data achieved by Materialise Mimics Research software. Nine months postoperative functional and esthetic result and radiological findings showed to be reasonable. That application of virtual simulation significantly allows to determine best direction of distraction and improves postoperative outcomes of surgical treatment of Crouzon syndrome.

No MeSH data available.


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Ophthalmological investigation of the patient revealed: (a) strabismus; (b) proptosis; (c) and (d) exophthalmos
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Figure 2: Ophthalmological investigation of the patient revealed: (a) strabismus; (b) proptosis; (c) and (d) exophthalmos

Mentions: A 20-year-old female has been admitted to the hospital with symptoms of facial and head dysmorphism, hypertelorism malocclusion, impaired speech and eating difficulties. Upon anamnesis certain pathology is congenital and first signs were noted immediately after birth. No specific treatment or diagnosis was done to the date. Clinical investigation revealed slight disproportion in head and trunk proportions; wide, flat and oblong forehead; expressed supraorbital ridge, short and wide face, beaked nose deformity. Intraoral investigation revealed Class III malocclusion, maxillary hypoplasia, dome-like deformity of the palate, abnormal anatomy of teeth, narrowing of the upper and lower dental arches [Figure 1]. Ophthalmological investigation detected strabismus, exophthalmos, proptosis [Figure 2].


Crouzon syndrome: Virtual planning of surgical treatment by application of internal distractors
Ophthalmological investigation of the patient revealed: (a) strabismus; (b) proptosis; (c) and (d) exophthalmos
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC4979330&req=5

Figure 2: Ophthalmological investigation of the patient revealed: (a) strabismus; (b) proptosis; (c) and (d) exophthalmos
Mentions: A 20-year-old female has been admitted to the hospital with symptoms of facial and head dysmorphism, hypertelorism malocclusion, impaired speech and eating difficulties. Upon anamnesis certain pathology is congenital and first signs were noted immediately after birth. No specific treatment or diagnosis was done to the date. Clinical investigation revealed slight disproportion in head and trunk proportions; wide, flat and oblong forehead; expressed supraorbital ridge, short and wide face, beaked nose deformity. Intraoral investigation revealed Class III malocclusion, maxillary hypoplasia, dome-like deformity of the palate, abnormal anatomy of teeth, narrowing of the upper and lower dental arches [Figure 1]. Ophthalmological investigation detected strabismus, exophthalmos, proptosis [Figure 2].

View Article: PubMed Central - PubMed

ABSTRACT

Crouzon syndrome is one of the frequent pathologies within craniosynostosis syndrome. Current progress in computers and biotechnologies allows improving surgical approach and forecasting final result of reconstruction as well. We present a case of successful surgical treatment of Crouzon syndrome, done by application of virtual planning allowing determining “monobloc” features, type of reconstruction and distraction protocol as well. A 20-year-old female had presented with craniofacial deformity. Clinical and radiological investigation revealed Crouzon syndrome. The “monobloc” creation, cranioplasty and internal distractors positioning, direction and schedule of advancement were done according to preoperative virtual planning data achieved by Materialise Mimics Research software. Nine months postoperative functional and esthetic result and radiological findings showed to be reasonable. That application of virtual simulation significantly allows to determine best direction of distraction and improves postoperative outcomes of surgical treatment of Crouzon syndrome.

No MeSH data available.


Related in: MedlinePlus