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Adult-onset cystic hygroma: A case report of rare entity.

Bahl S, Shah V, Anchlia S, Vyas S - Indian J Dent (2016 Jan-Mar)

Bottom Line: Patients presenting with a painless, soft, fluctuant, and enlarging neck mass should have a careful history and physical examination along with radiological imaging to assist with diagnosis.Surgical intervention is the treatment of choice for this rare condition.The objectives of this case report are to discuss the clinical presentation, diagnosis, histopathological findings and management of this malformation.

View Article: PubMed Central - PubMed

Affiliation: Department of Oral and Maxillofacial Pathology, K.M Shah Dental College, Sumandeep Vidyapeeth University, Vadodara, India.

ABSTRACT
Cystic hygroma is a benign congenital malformation of the lymphatic system that occurs in infant or children younger than 2 years of age. Although cystic hygroma is well recognized in pediatric practice, it seldom presents de novo in adulthood. These are commonly present in head and neck but can be present anywhere. Cystic hygroma is very rare in adults, but it should be considered in the differential diagnosis of adult neck swellings. Patients presenting with a painless, soft, fluctuant, and enlarging neck mass should have a careful history and physical examination along with radiological imaging to assist with diagnosis. Surgical intervention is the treatment of choice for this rare condition. Here, we are reporting a case of cystic hygroma in a 32-year-old male patient in the neck region. The objectives of this case report are to discuss the clinical presentation, diagnosis, histopathological findings and management of this malformation.

No MeSH data available.


Related in: MedlinePlus

(a) Cystic lobulated swelling present in the neck region. (b) Surgically excised specimen
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Figure 3: (a) Cystic lobulated swelling present in the neck region. (b) Surgically excised specimen

Mentions: The patient was taken under general anesthesia and Risdon's incision placed in the right submandibular region. The lesion was excised in toto [Figure 3a]. Macroscopically biopsy specimen [Figure 3b] was multiloculated measuring 4.8 cm × 1.8 cm × 1.5 cm. The biopsy specimen was soft in consistency with irregular borders, color was creamish pink. Microscopically specimen showed [Figure 4a] cystic lumen formed by cystically dilated vascular lymphatic channels containing pinkish eosinophilic proteinicious lymphatic fluid along with lymphoplasmacytic cell infiltration. Cystic lumen was lined by single flattened endothelium layer. The connective tissue wall [Figure 4b] was loosely fibroblastic with engorged capillaries, adipocytes and extravasated red blood cells. The final diagnosis correlating with clinical and radiological findings was made as adult-onset cystic hygroma. Postoperatively patient recovered well [Figure 5] without neurological symptoms. The patient is on regular follow-up of 1, 3, and 6 months.


Adult-onset cystic hygroma: A case report of rare entity.

Bahl S, Shah V, Anchlia S, Vyas S - Indian J Dent (2016 Jan-Mar)

(a) Cystic lobulated swelling present in the neck region. (b) Surgically excised specimen
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC4836099&req=5

Figure 3: (a) Cystic lobulated swelling present in the neck region. (b) Surgically excised specimen
Mentions: The patient was taken under general anesthesia and Risdon's incision placed in the right submandibular region. The lesion was excised in toto [Figure 3a]. Macroscopically biopsy specimen [Figure 3b] was multiloculated measuring 4.8 cm × 1.8 cm × 1.5 cm. The biopsy specimen was soft in consistency with irregular borders, color was creamish pink. Microscopically specimen showed [Figure 4a] cystic lumen formed by cystically dilated vascular lymphatic channels containing pinkish eosinophilic proteinicious lymphatic fluid along with lymphoplasmacytic cell infiltration. Cystic lumen was lined by single flattened endothelium layer. The connective tissue wall [Figure 4b] was loosely fibroblastic with engorged capillaries, adipocytes and extravasated red blood cells. The final diagnosis correlating with clinical and radiological findings was made as adult-onset cystic hygroma. Postoperatively patient recovered well [Figure 5] without neurological symptoms. The patient is on regular follow-up of 1, 3, and 6 months.

Bottom Line: Patients presenting with a painless, soft, fluctuant, and enlarging neck mass should have a careful history and physical examination along with radiological imaging to assist with diagnosis.Surgical intervention is the treatment of choice for this rare condition.The objectives of this case report are to discuss the clinical presentation, diagnosis, histopathological findings and management of this malformation.

View Article: PubMed Central - PubMed

Affiliation: Department of Oral and Maxillofacial Pathology, K.M Shah Dental College, Sumandeep Vidyapeeth University, Vadodara, India.

ABSTRACT
Cystic hygroma is a benign congenital malformation of the lymphatic system that occurs in infant or children younger than 2 years of age. Although cystic hygroma is well recognized in pediatric practice, it seldom presents de novo in adulthood. These are commonly present in head and neck but can be present anywhere. Cystic hygroma is very rare in adults, but it should be considered in the differential diagnosis of adult neck swellings. Patients presenting with a painless, soft, fluctuant, and enlarging neck mass should have a careful history and physical examination along with radiological imaging to assist with diagnosis. Surgical intervention is the treatment of choice for this rare condition. Here, we are reporting a case of cystic hygroma in a 32-year-old male patient in the neck region. The objectives of this case report are to discuss the clinical presentation, diagnosis, histopathological findings and management of this malformation.

No MeSH data available.


Related in: MedlinePlus