Specular microscopy in OD.Abbreviation: OD, right eye.

Retinitis pigmentosa with concomitant essential iris atrophy and glaucoma - case report. Meirelles SH, Barreto AS, Buscacio ES, Shinzato E, Patrão LF, de Oliveira Silva MS - Clin Ophthalmol (2015) Bottom Line: To report a case of a young patient with retinitis pigmentosa (RP), essential iris atrophy, and glaucoma.The patient presented glaucoma due to the iridocorneal endothelial syndrome, despite low age.RP is a bilateral disorder that may be associated with angle-closure glaucoma. View Article: PubMed Central - PubMed Affiliation: Piedade Municipal Hospital, Rio de Janeiro, Brazil ; Federal University of Rio de Janeiro, Brazil ; Estacio de Sá University, Rio de Janeiro, Brazil. ABSTRACT Purpose: To report a case of a young patient with retinitis pigmentosa (RP), essential iris atrophy, and glaucoma. Case report: This report presents a case of a 22-year-old female patient with unilateral glaucoma, increased intraocular pressure, increased cup-disc ratio, iris atrophy, peripheral anterior synechiae, and bilateral RP. Discussion: The patient presented glaucoma due to the iridocorneal endothelial syndrome, despite low age. RP is a bilateral disorder that may be associated with angle-closure glaucoma. No MeSH data available. Related in: MedlinePlus	© Copyright Policy Related In: Results - Collection License Show All Figures getmorefigures.php?uid=PMC4664549&req=5 f10-opth-9-2139: Specular microscopy in OD.Abbreviation: OD, right eye. Mentions: In the ophthalmic examination, the best-corrected visual acuity was OD: 20/50 (−1,00 cyl ×115) and left eye (OS): 20/25 (+2,00 sph −1,00 cyl ×10). The slit lamp examination showed multiple iris holes and corectopia in OD (Figures 1 and 2), clear cornea in both eyes (OU), and no alterations in OS. IOP by Goldmann applanation tonometry was OD: 34 mmHg and OS: 16 mmHg at 3 pm. The gonioscopy revealed 360° isolated peripheral anterior synechiae in OD (Figure 3) and a visible open-angle up to ciliary body in OS. The fundoscopy (Figures 4 and 5) presented cup–disc ratio 0.9 vertical (V) ×0.9 horizontal (H), visible lamina cribrosa pores, preserved macula, and peripheral pigment mobilization in OD. In OS, the fundoscopy revealed cup–disc ratio 0.3 V ×0.3 H, preserved macula, and peripheral pigment mobilization. The automated perimetry (Figures 6 and 7) and manual perimetry (Figures 8 and 9) showed central island vision in OD and ring scotoma in OS. The ultrasound pachymetry was 524 µm and 530 µm in OD and OS, respectively. The specular microscopy revealed pleomorphism and polymegathism in OU (Figures 10 and 11). Fluorescein angiography featured blocked fluorescence in the peripheral pigment mobilization areas in OU.

Retinitis pigmentosa with concomitant essential iris atrophy and glaucoma - case report.

Meirelles SH, Barreto AS, Buscacio ES, Shinzato E, Patrão LF, de Oliveira Silva MS - Clin Ophthalmol (2015)

Bottom Line: To report a case of a young patient with retinitis pigmentosa (RP), essential iris atrophy, and glaucoma.The patient presented glaucoma due to the iridocorneal endothelial syndrome, despite low age.RP is a bilateral disorder that may be associated with angle-closure glaucoma.

View Article: PubMed Central - PubMed

Affiliation: Piedade Municipal Hospital, Rio de Janeiro, Brazil ; Federal University of Rio de Janeiro, Brazil ; Estacio de Sá University, Rio de Janeiro, Brazil.

ABSTRACT

Purpose: To report a case of a young patient with retinitis pigmentosa (RP), essential iris atrophy, and glaucoma.

Case report: This report presents a case of a 22-year-old female patient with unilateral glaucoma, increased intraocular pressure, increased cup-disc ratio, iris atrophy, peripheral anterior synechiae, and bilateral RP.

Discussion: The patient presented glaucoma due to the iridocorneal endothelial syndrome, despite low age. RP is a bilateral disorder that may be associated with angle-closure glaucoma.

No MeSH data available.

Related in: MedlinePlus

Specular microscopy in OD.Abbreviation: OD, right eye.

Related In: Results - Collection

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f10-opth-9-2139: Specular microscopy in OD.Abbreviation: OD, right eye.

Mentions: In the ophthalmic examination, the best-corrected visual acuity was OD: 20/50 (−1,00 cyl ×115) and left eye (OS): 20/25 (+2,00 sph −1,00 cyl ×10). The slit lamp examination showed multiple iris holes and corectopia in OD (Figures 1 and 2), clear cornea in both eyes (OU), and no alterations in OS. IOP by Goldmann applanation tonometry was OD: 34 mmHg and OS: 16 mmHg at 3 pm. The gonioscopy revealed 360° isolated peripheral anterior synechiae in OD (Figure 3) and a visible open-angle up to ciliary body in OS. The fundoscopy (Figures 4 and 5) presented cup–disc ratio 0.9 vertical (V) ×0.9 horizontal (H), visible lamina cribrosa pores, preserved macula, and peripheral pigment mobilization in OD. In OS, the fundoscopy revealed cup–disc ratio 0.3 V ×0.3 H, preserved macula, and peripheral pigment mobilization. The automated perimetry (Figures 6 and 7) and manual perimetry (Figures 8 and 9) showed central island vision in OD and ring scotoma in OS. The ultrasound pachymetry was 524 µm and 530 µm in OD and OS, respectively. The specular microscopy revealed pleomorphism and polymegathism in OU (Figures 10 and 11). Fluorescein angiography featured blocked fluorescence in the peripheral pigment mobilization areas in OU.