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Pycnodysostosis with Special Emphasis on Dentofacial Characteristics.

Khoja A, Fida M, Shaikh A - Case Rep Dent (2015)

Bottom Line: Dental surgeons should be aware of the limitations and possible adverse oral complications such as osteomyelitis of bone in these patients.This will guide them in planning realistic treatment goals.The aim of this case report is to give an insight into the etiology, pathogenesis, and differential diagnosis of this disorder and to prepare the dentists and maxillofacial surgeons to overcome the challenges in treating these patients.

View Article: PubMed Central - PubMed

Affiliation: Section of Dentistry, Department of Surgery, The Aga Khan University Hospital, Stadium Road, P.O. Box 3500, Karachi 74800, Pakistan.

ABSTRACT
Pycnodysostosis is an autosomal recessive disorder that manifests as osteosclerosis of the skeleton due to the defective osteoclasts mediated bone turnover. The diagnosis of this disorder is established on the basis of its characteristic features and must be differentially diagnosed with other bone disorders. Dental surgeons should be aware of the limitations and possible adverse oral complications such as osteomyelitis of bone in these patients. This will guide them in planning realistic treatment goals. This paper reports the clinical and radiographic features of pycnodysostosis with the great emphasis on its dentofacial characteristics. The aim of this case report is to give an insight into the etiology, pathogenesis, and differential diagnosis of this disorder and to prepare the dentists and maxillofacial surgeons to overcome the challenges in treating these patients.

No MeSH data available.


Related in: MedlinePlus

Treatment progress after maxillary orthopedic expansion.
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fig7: Treatment progress after maxillary orthopedic expansion.

Mentions: The treatment plan decided for this patient comprised cemented upper bonded expander with the midline expansion screw which was activated 0.25 mm every alternate day using a slow expansion technique. The follow-up visits were scheduled every month to assess the overall treatment progress and radiographs were taken to see any adverse effects. Periodic scaling and polishing of teeth were carried out to maintain the oral hygiene. Meticulous attention was given on any carious lesions, white spot lesions, plaque, or calculus deposits that may arise during the course of treatment. The total duration to achieve desired orthopedic expansion was 6 months. The appliance was kept passive for the next two months to allow remodeling of tissues. Following the slow expansion technique, the next step followed was leveling and alignment of the maxillary teeth with comprehensive fixed mechanotherapy using Roth prescription 0.022 slot (Figure 7). At present, space creation for right and left maxillary second premolars is being performed using the push coil springs mechanics. Once the gross alignment of maxillary dentition is achieved, mandibular teeth will be bonded. Further treatment plan includes extractions of third molars and right mandibular lateral incisor under general anesthesia, active distalization of right upper first permanent molar, and uprighting of mandibular second permanent molars utilizing mini implant anchorage. The purpose of the entire orthodontic treatment is to achieve normal overjet, overbite, and Class I buccal occlusion and to provide optimal function and improved esthetics.


Pycnodysostosis with Special Emphasis on Dentofacial Characteristics.

Khoja A, Fida M, Shaikh A - Case Rep Dent (2015)

Treatment progress after maxillary orthopedic expansion.
© Copyright Policy
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC4663328&req=5

fig7: Treatment progress after maxillary orthopedic expansion.
Mentions: The treatment plan decided for this patient comprised cemented upper bonded expander with the midline expansion screw which was activated 0.25 mm every alternate day using a slow expansion technique. The follow-up visits were scheduled every month to assess the overall treatment progress and radiographs were taken to see any adverse effects. Periodic scaling and polishing of teeth were carried out to maintain the oral hygiene. Meticulous attention was given on any carious lesions, white spot lesions, plaque, or calculus deposits that may arise during the course of treatment. The total duration to achieve desired orthopedic expansion was 6 months. The appliance was kept passive for the next two months to allow remodeling of tissues. Following the slow expansion technique, the next step followed was leveling and alignment of the maxillary teeth with comprehensive fixed mechanotherapy using Roth prescription 0.022 slot (Figure 7). At present, space creation for right and left maxillary second premolars is being performed using the push coil springs mechanics. Once the gross alignment of maxillary dentition is achieved, mandibular teeth will be bonded. Further treatment plan includes extractions of third molars and right mandibular lateral incisor under general anesthesia, active distalization of right upper first permanent molar, and uprighting of mandibular second permanent molars utilizing mini implant anchorage. The purpose of the entire orthodontic treatment is to achieve normal overjet, overbite, and Class I buccal occlusion and to provide optimal function and improved esthetics.

Bottom Line: Dental surgeons should be aware of the limitations and possible adverse oral complications such as osteomyelitis of bone in these patients.This will guide them in planning realistic treatment goals.The aim of this case report is to give an insight into the etiology, pathogenesis, and differential diagnosis of this disorder and to prepare the dentists and maxillofacial surgeons to overcome the challenges in treating these patients.

View Article: PubMed Central - PubMed

Affiliation: Section of Dentistry, Department of Surgery, The Aga Khan University Hospital, Stadium Road, P.O. Box 3500, Karachi 74800, Pakistan.

ABSTRACT
Pycnodysostosis is an autosomal recessive disorder that manifests as osteosclerosis of the skeleton due to the defective osteoclasts mediated bone turnover. The diagnosis of this disorder is established on the basis of its characteristic features and must be differentially diagnosed with other bone disorders. Dental surgeons should be aware of the limitations and possible adverse oral complications such as osteomyelitis of bone in these patients. This will guide them in planning realistic treatment goals. This paper reports the clinical and radiographic features of pycnodysostosis with the great emphasis on its dentofacial characteristics. The aim of this case report is to give an insight into the etiology, pathogenesis, and differential diagnosis of this disorder and to prepare the dentists and maxillofacial surgeons to overcome the challenges in treating these patients.

No MeSH data available.


Related in: MedlinePlus