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Extrarenal nephroblastoma.

Apoznański W, Sawicz-Birkowska K, Palczewski M, Szydełko T - Cent European J Urol (2015)

Bottom Line: What can be defined as extrarenal Wilms' tumor must satisfy the following criteria: histologically confirmed nephroblastoma and extrarenal location.The retroperineal location is reported to be typical in males, whereas the inguinal region is believed to predominate in females.In absence of typical clinical presentation or conclusive imaging tests, the diagnosis is based on histology after the resection of the tumor.

View Article: PubMed Central - PubMed

Affiliation: Department of Pediatric Surgery and Urology, Medical University, Wrocław, Poland.

ABSTRACT

Introduction: Nephroblastoma is one of the most common solid tumours in children. The occurrence of extrarenal nephroblastoma is exceedingly rare. What can be defined as extrarenal Wilms' tumor must satisfy the following criteria: histologically confirmed nephroblastoma and extrarenal location.

Material and methods: Current data on extrarenal nephroblastoma based on a selective review of the literature.

Results: The retroperineal location is reported to be typical in males, whereas the inguinal region is believed to predominate in females. There are no characteristic manifestations of extrarenal nephroblastoma. The symptoms depend on the location and stage upon diagnosis. US, CT and MRI are used to detect tumours in the retroperiteneal space, inguinal, sacro-coccal and scrotal area. However, extrarenal nephroblastoma does not show characteristic radiological features.

Conclusions: In absence of typical clinical presentation or conclusive imaging tests, the diagnosis is based on histology after the resection of the tumor. The recommended management of the extrarenal nephroblastoma is similar to the treatment of intrarenal nephroblastoma.

No MeSH data available.


Related in: MedlinePlus

Large palpable mass of the abdomen.
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Figure 0001: Large palpable mass of the abdomen.

Mentions: There are no characteristic manifestations of extrarenal nephroblastoma. The symptoms depend on the location and stage upon diagnosis. The most common presentation is nonspecific abdominal pain and, as in the case of intrarenal nephroblastoma, a palpable mass (Figure 1). Pelvic and retroperitoneal location is associated with gastrointestinal disorders, cachexia, haematuria, gynaecological haemorrhage and in few patients even raised temperature. The clinical presentation depends mainly on the tumor size [3, 4, 12, 22–24].


Extrarenal nephroblastoma.

Apoznański W, Sawicz-Birkowska K, Palczewski M, Szydełko T - Cent European J Urol (2015)

Large palpable mass of the abdomen.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC4526617&req=5

Figure 0001: Large palpable mass of the abdomen.
Mentions: There are no characteristic manifestations of extrarenal nephroblastoma. The symptoms depend on the location and stage upon diagnosis. The most common presentation is nonspecific abdominal pain and, as in the case of intrarenal nephroblastoma, a palpable mass (Figure 1). Pelvic and retroperitoneal location is associated with gastrointestinal disorders, cachexia, haematuria, gynaecological haemorrhage and in few patients even raised temperature. The clinical presentation depends mainly on the tumor size [3, 4, 12, 22–24].

Bottom Line: What can be defined as extrarenal Wilms' tumor must satisfy the following criteria: histologically confirmed nephroblastoma and extrarenal location.The retroperineal location is reported to be typical in males, whereas the inguinal region is believed to predominate in females.In absence of typical clinical presentation or conclusive imaging tests, the diagnosis is based on histology after the resection of the tumor.

View Article: PubMed Central - PubMed

Affiliation: Department of Pediatric Surgery and Urology, Medical University, Wrocław, Poland.

ABSTRACT

Introduction: Nephroblastoma is one of the most common solid tumours in children. The occurrence of extrarenal nephroblastoma is exceedingly rare. What can be defined as extrarenal Wilms' tumor must satisfy the following criteria: histologically confirmed nephroblastoma and extrarenal location.

Material and methods: Current data on extrarenal nephroblastoma based on a selective review of the literature.

Results: The retroperineal location is reported to be typical in males, whereas the inguinal region is believed to predominate in females. There are no characteristic manifestations of extrarenal nephroblastoma. The symptoms depend on the location and stage upon diagnosis. US, CT and MRI are used to detect tumours in the retroperiteneal space, inguinal, sacro-coccal and scrotal area. However, extrarenal nephroblastoma does not show characteristic radiological features.

Conclusions: In absence of typical clinical presentation or conclusive imaging tests, the diagnosis is based on histology after the resection of the tumor. The recommended management of the extrarenal nephroblastoma is similar to the treatment of intrarenal nephroblastoma.

No MeSH data available.


Related in: MedlinePlus