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Fetal Magnetic Resonance Imaging of Malformations Associated with Heterotaxy.

Loomba R, Shah PH, Anderson RH - Cureus (2015)

Bottom Line: One such syndrome is so-called "visceral heterotaxy", in which there is typically an isomeric, rather than a lateralized, arrangement of the thoracic and abdominal organs.Typically associated with complex congenital cardiac malformations, heterotaxy can also involve the central nervous system, and produce pulmonary, gastrointestinal, immunologic, and genitourinary malformations.In this review, we discuss how these findings can be demonstrated using fetal MRI.

View Article: PubMed Central - HTML - PubMed

Affiliation: Cardiology Dept., Children's Hospital of Wisconsin.

ABSTRACT
Magnetic resonance imaging (MRI) is increasingly used as an investigation during fetal life, particularly for assessment of intracranial masses, congenital diaphragmatic hernia, myelomeningocele, and abdominal masses. As the number of scans increases, so is the variety of congenital malformations being recognized. It is axiomatic that interpretation of the findings is enhanced when attention is paid to the likely findings in the setting of known syndromes, this information then dictating the need for additional acquisition of images. One such syndrome is so-called "visceral heterotaxy", in which there is typically an isomeric, rather than a lateralized, arrangement of the thoracic and abdominal organs. Typically associated with complex congenital cardiac malformations, heterotaxy can also involve the central nervous system, and produce pulmonary, gastrointestinal, immunologic, and genitourinary malformations. In this review, we discuss how these findings can be demonstrated using fetal MRI.

No MeSH data available.


Related in: MedlinePlus

Multicystic kidneyT2-weighted HASTE imaging of monochorionic, monoamniotic twins. Panel A demonstrates the affected twin is on the right with a thickened and distended bladder. Panel B is an axial slice demonstrating a multicystic kidney (arrow). Reprinted without change from Bischoff, et al. under the creative commons license
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FIG19: Multicystic kidneyT2-weighted HASTE imaging of monochorionic, monoamniotic twins. Panel A demonstrates the affected twin is on the right with a thickened and distended bladder. Panel B is an axial slice demonstrating a multicystic kidney (arrow). Reprinted without change from Bischoff, et al. under the creative commons license

Mentions: Heterotaxy is associated with malformations of the genitourinary system, including horseshoe kidney (Figure 16), ectopic ureters, ureteral duplication, cystic kidneys (Figures 1, 19), solitary kidney, and cloacal duplication [58, 62-63]. These malformations may be assessed using the fetal body protocol outlined above, although all stacks should be extended to include the fetal pelvis.


Fetal Magnetic Resonance Imaging of Malformations Associated with Heterotaxy.

Loomba R, Shah PH, Anderson RH - Cureus (2015)

Multicystic kidneyT2-weighted HASTE imaging of monochorionic, monoamniotic twins. Panel A demonstrates the affected twin is on the right with a thickened and distended bladder. Panel B is an axial slice demonstrating a multicystic kidney (arrow). Reprinted without change from Bischoff, et al. under the creative commons license
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC4494530&req=5

FIG19: Multicystic kidneyT2-weighted HASTE imaging of monochorionic, monoamniotic twins. Panel A demonstrates the affected twin is on the right with a thickened and distended bladder. Panel B is an axial slice demonstrating a multicystic kidney (arrow). Reprinted without change from Bischoff, et al. under the creative commons license
Mentions: Heterotaxy is associated with malformations of the genitourinary system, including horseshoe kidney (Figure 16), ectopic ureters, ureteral duplication, cystic kidneys (Figures 1, 19), solitary kidney, and cloacal duplication [58, 62-63]. These malformations may be assessed using the fetal body protocol outlined above, although all stacks should be extended to include the fetal pelvis.

Bottom Line: One such syndrome is so-called "visceral heterotaxy", in which there is typically an isomeric, rather than a lateralized, arrangement of the thoracic and abdominal organs.Typically associated with complex congenital cardiac malformations, heterotaxy can also involve the central nervous system, and produce pulmonary, gastrointestinal, immunologic, and genitourinary malformations.In this review, we discuss how these findings can be demonstrated using fetal MRI.

View Article: PubMed Central - HTML - PubMed

Affiliation: Cardiology Dept., Children's Hospital of Wisconsin.

ABSTRACT
Magnetic resonance imaging (MRI) is increasingly used as an investigation during fetal life, particularly for assessment of intracranial masses, congenital diaphragmatic hernia, myelomeningocele, and abdominal masses. As the number of scans increases, so is the variety of congenital malformations being recognized. It is axiomatic that interpretation of the findings is enhanced when attention is paid to the likely findings in the setting of known syndromes, this information then dictating the need for additional acquisition of images. One such syndrome is so-called "visceral heterotaxy", in which there is typically an isomeric, rather than a lateralized, arrangement of the thoracic and abdominal organs. Typically associated with complex congenital cardiac malformations, heterotaxy can also involve the central nervous system, and produce pulmonary, gastrointestinal, immunologic, and genitourinary malformations. In this review, we discuss how these findings can be demonstrated using fetal MRI.

No MeSH data available.


Related in: MedlinePlus