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Fenestration of liver cysts in polycystic liver disease to improve quality of life: a case report and literature review.

Jung DH, Hwang S, Ahn CS, Moon DB, Song GW, Kim KH, Ha TY, Park GC, Lee SG - Korean J Hepatobiliary Pancreat Surg (2015)

Bottom Line: Multiple cysts in the enlarged liver were opened and the cyst walls were excised with electrocautery.The total liver volume was 3,870 ml before surgery and 3,125 ml at 1 week after surgery, showing a volume reduction of 19.3%.After surgery, her performance status improved significantly.

View Article: PubMed Central - PubMed

Affiliation: Division of Hepatobiliary Surgery and Liver Transplantation, Department of Surgery, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea.

ABSTRACT
Polycystic liver disease (PCLD) is characterized by a large number of liver cysts scattered throughout the liver parenchyma. We herein intend to present the beneficial effect of palliative fenestration treatment on quality of life in a patient with symptomatic PCLD. A 48-year-old female patient had been followed up for 5 years for both polycystic liver and kidney diseases at another institution. During follow-up for last 1 year, we recognized that she had barely maintained her ability of function in daily activities due to progressive worsening of fatigue and dyspnea on exertion. The patient finally underwent surgical fenestration treatment. Multiple cysts in the enlarged liver were opened and the cyst walls were excised with electrocautery. No surgical complication occurred and the patient was discharged 10 days after the open fenestration surgery. The total liver volume was 3,870 ml before surgery and 3,125 ml at 1 week after surgery, showing a volume reduction of 19.3%. After surgery, her performance status improved significantly. In the present case, significant improvement in quality of life and daily activity performance was achieved after open fenestration treatment over 18 months of follow-up without disease recurrence.

No MeSH data available.


Related in: MedlinePlus

Computed tomography follow-up of the abdomen. Multiple distended cysts occupied the liver just before surgery (A); Cyst size was significantly reduced 1 week after fenestration surgery (B); No increase in the size of liver cysts was observed in the 6-month (C) and 18-month (D) images. Because of improvement in the nutritional status, subcutaneous fat was thickened in the 18-month image (D).
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Figure 5: Computed tomography follow-up of the abdomen. Multiple distended cysts occupied the liver just before surgery (A); Cyst size was significantly reduced 1 week after fenestration surgery (B); No increase in the size of liver cysts was observed in the 6-month (C) and 18-month (D) images. Because of improvement in the nutritional status, subcutaneous fat was thickened in the 18-month image (D).

Mentions: At 1 month after surgery, ECOG performance status improved to 1 and the GIQLI score was significantly increased to 122. During regular follow-up at an interval of 6 months, follow-up CT showed no progression in cyst size and flat abdomen was observed (Fig. 5). After 1 year, ECOG performance status improved to 0 but the GIQLI score was slightly decreased to 114. The patient is doing well and she is performing her normal activities at 18 months after surgery with no evidence of disease recurrence.


Fenestration of liver cysts in polycystic liver disease to improve quality of life: a case report and literature review.

Jung DH, Hwang S, Ahn CS, Moon DB, Song GW, Kim KH, Ha TY, Park GC, Lee SG - Korean J Hepatobiliary Pancreat Surg (2015)

Computed tomography follow-up of the abdomen. Multiple distended cysts occupied the liver just before surgery (A); Cyst size was significantly reduced 1 week after fenestration surgery (B); No increase in the size of liver cysts was observed in the 6-month (C) and 18-month (D) images. Because of improvement in the nutritional status, subcutaneous fat was thickened in the 18-month image (D).
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC4494095&req=5

Figure 5: Computed tomography follow-up of the abdomen. Multiple distended cysts occupied the liver just before surgery (A); Cyst size was significantly reduced 1 week after fenestration surgery (B); No increase in the size of liver cysts was observed in the 6-month (C) and 18-month (D) images. Because of improvement in the nutritional status, subcutaneous fat was thickened in the 18-month image (D).
Mentions: At 1 month after surgery, ECOG performance status improved to 1 and the GIQLI score was significantly increased to 122. During regular follow-up at an interval of 6 months, follow-up CT showed no progression in cyst size and flat abdomen was observed (Fig. 5). After 1 year, ECOG performance status improved to 0 but the GIQLI score was slightly decreased to 114. The patient is doing well and she is performing her normal activities at 18 months after surgery with no evidence of disease recurrence.

Bottom Line: Multiple cysts in the enlarged liver were opened and the cyst walls were excised with electrocautery.The total liver volume was 3,870 ml before surgery and 3,125 ml at 1 week after surgery, showing a volume reduction of 19.3%.After surgery, her performance status improved significantly.

View Article: PubMed Central - PubMed

Affiliation: Division of Hepatobiliary Surgery and Liver Transplantation, Department of Surgery, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea.

ABSTRACT
Polycystic liver disease (PCLD) is characterized by a large number of liver cysts scattered throughout the liver parenchyma. We herein intend to present the beneficial effect of palliative fenestration treatment on quality of life in a patient with symptomatic PCLD. A 48-year-old female patient had been followed up for 5 years for both polycystic liver and kidney diseases at another institution. During follow-up for last 1 year, we recognized that she had barely maintained her ability of function in daily activities due to progressive worsening of fatigue and dyspnea on exertion. The patient finally underwent surgical fenestration treatment. Multiple cysts in the enlarged liver were opened and the cyst walls were excised with electrocautery. No surgical complication occurred and the patient was discharged 10 days after the open fenestration surgery. The total liver volume was 3,870 ml before surgery and 3,125 ml at 1 week after surgery, showing a volume reduction of 19.3%. After surgery, her performance status improved significantly. In the present case, significant improvement in quality of life and daily activity performance was achieved after open fenestration treatment over 18 months of follow-up without disease recurrence.

No MeSH data available.


Related in: MedlinePlus