Limits...
Extranodal Rosai-Dorfman Disease Involving the Left Atrium: Cardiac MRI, CT, and PET Scan Findings.

Daruwalla VJ, Parekh K, Tahir H, Collins JD, Carr J - Case Rep Radiol (2015)

Bottom Line: Rosai-Dorfman disease (RDD) is a rare entity that usually involves the lymph nodes but extranodal involvements have been seen in numerous cases, although RDD with cardiovascular involvement is extremely rare.We describe a case of a young male who presented with intermittent palpitations and was found to have a left atrium mass.RDD should be considered as one of the differentials even for isolated cardiac lesions.

View Article: PubMed Central - PubMed

Affiliation: Conemaugh Memorial Hospital/Temple University, 1199 Mckinley Avenue, Johnstown, PA 15905, USA.

ABSTRACT
Rosai-Dorfman disease (RDD) is a rare entity that usually involves the lymph nodes but extranodal involvements have been seen in numerous cases, although RDD with cardiovascular involvement is extremely rare. We describe a case of a young male who presented with intermittent palpitations and was found to have a left atrium mass. Our case not only emphasizes the rarity of the above lesion but also highlights the importance of modern-day imaging like computed tomography, Cardiac Magnetic Resonance Imaging (CMRI), and PET scan in characterizing such nonspecific lesions and directing appropriate line of treatment. RDD should be considered as one of the differentials even for isolated cardiac lesions.

No MeSH data available.


Related in: MedlinePlus

Prospectively ECG gated CT chest with contrast. Hypodense mass in left atrium is well demonstrated on coronal reconstructed images (a). CT scan helps in assessment of any possible compression of adjacent structures by mass lesion. Narrowing of left superior pulmonary vein is seen on axial image (b and d). Sagittal reconstructed image shows hypodense soft tissue thickening along the undersurface of arch of aorta that represents mediastinal lymphadenopathy (c).
© Copyright Policy - open-access
Related In: Results  -  Collection


getmorefigures.php?uid=PMC4477210&req=5

fig3: Prospectively ECG gated CT chest with contrast. Hypodense mass in left atrium is well demonstrated on coronal reconstructed images (a). CT scan helps in assessment of any possible compression of adjacent structures by mass lesion. Narrowing of left superior pulmonary vein is seen on axial image (b and d). Sagittal reconstructed image shows hypodense soft tissue thickening along the undersurface of arch of aorta that represents mediastinal lymphadenopathy (c).

Mentions: Patient was further evaluated with Computed Tomography Angiography (CTA) of chest for better anatomical evaluation of the mass, which confirmed a cardiac region mass which is difficult to distinguish from the mediastinum and is located at the roof and posterior superior wall of the left atrium similar to the description on the CMRI (Figure 3). The mass demonstrated an infiltrative appearance and may actually originate in the mediastinum, exerting mass effect on to the left atrium. Based on findings of MR and CT, possibility of lymphoproliferative disorder was the primary consideration. PET scan was done to further validate the diagnosis.


Extranodal Rosai-Dorfman Disease Involving the Left Atrium: Cardiac MRI, CT, and PET Scan Findings.

Daruwalla VJ, Parekh K, Tahir H, Collins JD, Carr J - Case Rep Radiol (2015)

Prospectively ECG gated CT chest with contrast. Hypodense mass in left atrium is well demonstrated on coronal reconstructed images (a). CT scan helps in assessment of any possible compression of adjacent structures by mass lesion. Narrowing of left superior pulmonary vein is seen on axial image (b and d). Sagittal reconstructed image shows hypodense soft tissue thickening along the undersurface of arch of aorta that represents mediastinal lymphadenopathy (c).
© Copyright Policy - open-access
Related In: Results  -  Collection

Show All Figures
getmorefigures.php?uid=PMC4477210&req=5

fig3: Prospectively ECG gated CT chest with contrast. Hypodense mass in left atrium is well demonstrated on coronal reconstructed images (a). CT scan helps in assessment of any possible compression of adjacent structures by mass lesion. Narrowing of left superior pulmonary vein is seen on axial image (b and d). Sagittal reconstructed image shows hypodense soft tissue thickening along the undersurface of arch of aorta that represents mediastinal lymphadenopathy (c).
Mentions: Patient was further evaluated with Computed Tomography Angiography (CTA) of chest for better anatomical evaluation of the mass, which confirmed a cardiac region mass which is difficult to distinguish from the mediastinum and is located at the roof and posterior superior wall of the left atrium similar to the description on the CMRI (Figure 3). The mass demonstrated an infiltrative appearance and may actually originate in the mediastinum, exerting mass effect on to the left atrium. Based on findings of MR and CT, possibility of lymphoproliferative disorder was the primary consideration. PET scan was done to further validate the diagnosis.

Bottom Line: Rosai-Dorfman disease (RDD) is a rare entity that usually involves the lymph nodes but extranodal involvements have been seen in numerous cases, although RDD with cardiovascular involvement is extremely rare.We describe a case of a young male who presented with intermittent palpitations and was found to have a left atrium mass.RDD should be considered as one of the differentials even for isolated cardiac lesions.

View Article: PubMed Central - PubMed

Affiliation: Conemaugh Memorial Hospital/Temple University, 1199 Mckinley Avenue, Johnstown, PA 15905, USA.

ABSTRACT
Rosai-Dorfman disease (RDD) is a rare entity that usually involves the lymph nodes but extranodal involvements have been seen in numerous cases, although RDD with cardiovascular involvement is extremely rare. We describe a case of a young male who presented with intermittent palpitations and was found to have a left atrium mass. Our case not only emphasizes the rarity of the above lesion but also highlights the importance of modern-day imaging like computed tomography, Cardiac Magnetic Resonance Imaging (CMRI), and PET scan in characterizing such nonspecific lesions and directing appropriate line of treatment. RDD should be considered as one of the differentials even for isolated cardiac lesions.

No MeSH data available.


Related in: MedlinePlus