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Extranodal Rosai-Dorfman Disease Involving the Left Atrium: Cardiac MRI, CT, and PET Scan Findings.

Daruwalla VJ, Parekh K, Tahir H, Collins JD, Carr J - Case Rep Radiol (2015)

Bottom Line: Rosai-Dorfman disease (RDD) is a rare entity that usually involves the lymph nodes but extranodal involvements have been seen in numerous cases, although RDD with cardiovascular involvement is extremely rare.We describe a case of a young male who presented with intermittent palpitations and was found to have a left atrium mass.RDD should be considered as one of the differentials even for isolated cardiac lesions.

View Article: PubMed Central - PubMed

Affiliation: Conemaugh Memorial Hospital/Temple University, 1199 Mckinley Avenue, Johnstown, PA 15905, USA.

ABSTRACT
Rosai-Dorfman disease (RDD) is a rare entity that usually involves the lymph nodes but extranodal involvements have been seen in numerous cases, although RDD with cardiovascular involvement is extremely rare. We describe a case of a young male who presented with intermittent palpitations and was found to have a left atrium mass. Our case not only emphasizes the rarity of the above lesion but also highlights the importance of modern-day imaging like computed tomography, Cardiac Magnetic Resonance Imaging (CMRI), and PET scan in characterizing such nonspecific lesions and directing appropriate line of treatment. RDD should be considered as one of the differentials even for isolated cardiac lesions.

No MeSH data available.


Related in: MedlinePlus

CMR—steady-state-free precession. Left atrial mass with infiltration of wall of left atrium in the form of wall thickening and postcontrast enhancement is seen on coronal steady-state-free precession images (a and b). Also seen is soft tissue mass in mediastinum with signal characteristics similar to left atrial mass. Precontrast 2-chamber view shows mass appearing isointense to left ventricular myocardium (c).
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fig2: CMR—steady-state-free precession. Left atrial mass with infiltration of wall of left atrium in the form of wall thickening and postcontrast enhancement is seen on coronal steady-state-free precession images (a and b). Also seen is soft tissue mass in mediastinum with signal characteristics similar to left atrial mass. Precontrast 2-chamber view shows mass appearing isointense to left ventricular myocardium (c).

Mentions: A 27-year-old African American male without any significant past medical history presented with intermittent palpitations and left ventricular hypertrophy on electrocardiogram (ECG). Two-dimensional (2D) transthoracic echocardiography showed an echodense mass in the left atrium. Further evaluation with Cardiac Magnetic Resonance Imaging (CMRI) demonstrated a heterogeneous broad base mass arising from the posterior superior wall and roof of the left atrium. The mass was located approximately at the expected location of coumadin ridge and measured 1.9 × 1.5 cm and demonstrated mild postcontrast enhancement (Figure 2). It arises from a diffusely thickened superior posterior wall and atrial roof but did not obstruct the pulmonary venous drainage at this time. Mediastinal lymphadenopathy with similar signal intensity as cardiac mass was noted on fat-suppressed postcontrast axial images (Figure 1). Lymphadenopathy was more marked in aortopulmonary region.


Extranodal Rosai-Dorfman Disease Involving the Left Atrium: Cardiac MRI, CT, and PET Scan Findings.

Daruwalla VJ, Parekh K, Tahir H, Collins JD, Carr J - Case Rep Radiol (2015)

CMR—steady-state-free precession. Left atrial mass with infiltration of wall of left atrium in the form of wall thickening and postcontrast enhancement is seen on coronal steady-state-free precession images (a and b). Also seen is soft tissue mass in mediastinum with signal characteristics similar to left atrial mass. Precontrast 2-chamber view shows mass appearing isointense to left ventricular myocardium (c).
© Copyright Policy - open-access
Related In: Results  -  Collection

Show All Figures
getmorefigures.php?uid=PMC4477210&req=5

fig2: CMR—steady-state-free precession. Left atrial mass with infiltration of wall of left atrium in the form of wall thickening and postcontrast enhancement is seen on coronal steady-state-free precession images (a and b). Also seen is soft tissue mass in mediastinum with signal characteristics similar to left atrial mass. Precontrast 2-chamber view shows mass appearing isointense to left ventricular myocardium (c).
Mentions: A 27-year-old African American male without any significant past medical history presented with intermittent palpitations and left ventricular hypertrophy on electrocardiogram (ECG). Two-dimensional (2D) transthoracic echocardiography showed an echodense mass in the left atrium. Further evaluation with Cardiac Magnetic Resonance Imaging (CMRI) demonstrated a heterogeneous broad base mass arising from the posterior superior wall and roof of the left atrium. The mass was located approximately at the expected location of coumadin ridge and measured 1.9 × 1.5 cm and demonstrated mild postcontrast enhancement (Figure 2). It arises from a diffusely thickened superior posterior wall and atrial roof but did not obstruct the pulmonary venous drainage at this time. Mediastinal lymphadenopathy with similar signal intensity as cardiac mass was noted on fat-suppressed postcontrast axial images (Figure 1). Lymphadenopathy was more marked in aortopulmonary region.

Bottom Line: Rosai-Dorfman disease (RDD) is a rare entity that usually involves the lymph nodes but extranodal involvements have been seen in numerous cases, although RDD with cardiovascular involvement is extremely rare.We describe a case of a young male who presented with intermittent palpitations and was found to have a left atrium mass.RDD should be considered as one of the differentials even for isolated cardiac lesions.

View Article: PubMed Central - PubMed

Affiliation: Conemaugh Memorial Hospital/Temple University, 1199 Mckinley Avenue, Johnstown, PA 15905, USA.

ABSTRACT
Rosai-Dorfman disease (RDD) is a rare entity that usually involves the lymph nodes but extranodal involvements have been seen in numerous cases, although RDD with cardiovascular involvement is extremely rare. We describe a case of a young male who presented with intermittent palpitations and was found to have a left atrium mass. Our case not only emphasizes the rarity of the above lesion but also highlights the importance of modern-day imaging like computed tomography, Cardiac Magnetic Resonance Imaging (CMRI), and PET scan in characterizing such nonspecific lesions and directing appropriate line of treatment. RDD should be considered as one of the differentials even for isolated cardiac lesions.

No MeSH data available.


Related in: MedlinePlus