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Familial gigantiform cementoma with Ehlers - Danlos syndrome: A report of 2 cases.

Şakar O, Aren G, Mumcu Z, Ünalan F, Aksakallı N, Tolgay CG - J Adv Prosthodont (2015)

Bottom Line: Ehlers-Danlos syndrome is an autosomal dominant hereditary disorder of connective tissue, while familial gigantiform cementoma is a condition that usually manifests as multiple radiopaque cementum-like masses throughout the jaws.This case report discusses the oral management and prosthetic rehabilitation of two patients presenting familial gigantiform cementoma with Ehlers-Danlos Syndrome.

View Article: PubMed Central - PubMed

Affiliation: Department of Prosthodontics, School of Dentistry, İstanbul University, İstanbul, Turkey.

ABSTRACT
Ehlers-Danlos syndrome is an autosomal dominant hereditary disorder of connective tissue, while familial gigantiform cementoma is a condition that usually manifests as multiple radiopaque cementum-like masses throughout the jaws. This case report discusses the oral management and prosthetic rehabilitation of two patients presenting familial gigantiform cementoma with Ehlers-Danlos Syndrome.

No MeSH data available.


Related in: MedlinePlus

(A) Extracted mandibular left first molar. (B) Microscopic view of tooth (loop magnification H&E). (C) Mineralized material (M) is observed surrounding the root and at the root apex (Ra) (×40, H&E).
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Figure 2: (A) Extracted mandibular left first molar. (B) Microscopic view of tooth (loop magnification H&E). (C) Mineralized material (M) is observed surrounding the root and at the root apex (Ra) (×40, H&E).

Mentions: After performing dental prophylaxis, teeth 36 and 46 were extracted because of severe infection and were evaluated histologically. The mineralized material showed apposition and resorption lines, and spherical mineralized tissue (large pulp stones) were free-floating within the pulp chamber (Fig. 2). Based on the clinical and histological findings, the patient was diagnosed with familial gigantiform cementoma with Ehlers-Danlos syndrome type VIII.


Familial gigantiform cementoma with Ehlers - Danlos syndrome: A report of 2 cases.

Şakar O, Aren G, Mumcu Z, Ünalan F, Aksakallı N, Tolgay CG - J Adv Prosthodont (2015)

(A) Extracted mandibular left first molar. (B) Microscopic view of tooth (loop magnification H&E). (C) Mineralized material (M) is observed surrounding the root and at the root apex (Ra) (×40, H&E).
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC4414950&req=5

Figure 2: (A) Extracted mandibular left first molar. (B) Microscopic view of tooth (loop magnification H&E). (C) Mineralized material (M) is observed surrounding the root and at the root apex (Ra) (×40, H&E).
Mentions: After performing dental prophylaxis, teeth 36 and 46 were extracted because of severe infection and were evaluated histologically. The mineralized material showed apposition and resorption lines, and spherical mineralized tissue (large pulp stones) were free-floating within the pulp chamber (Fig. 2). Based on the clinical and histological findings, the patient was diagnosed with familial gigantiform cementoma with Ehlers-Danlos syndrome type VIII.

Bottom Line: Ehlers-Danlos syndrome is an autosomal dominant hereditary disorder of connective tissue, while familial gigantiform cementoma is a condition that usually manifests as multiple radiopaque cementum-like masses throughout the jaws.This case report discusses the oral management and prosthetic rehabilitation of two patients presenting familial gigantiform cementoma with Ehlers-Danlos Syndrome.

View Article: PubMed Central - PubMed

Affiliation: Department of Prosthodontics, School of Dentistry, İstanbul University, İstanbul, Turkey.

ABSTRACT
Ehlers-Danlos syndrome is an autosomal dominant hereditary disorder of connective tissue, while familial gigantiform cementoma is a condition that usually manifests as multiple radiopaque cementum-like masses throughout the jaws. This case report discusses the oral management and prosthetic rehabilitation of two patients presenting familial gigantiform cementoma with Ehlers-Danlos Syndrome.

No MeSH data available.


Related in: MedlinePlus