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A new case of TEMPI syndrome.

Mohammadi F, Wolverson MK, Bastani B - Clin Kidney J (2012)

Bottom Line: We present an interesting case of a woman with new onset hypertension and abdominal fullness who was found to have huge bilateral perinephric fluid collections.Extensive workup revealed that she had secondary polycythemia, extensive truncal and proximal extremities telangiectasia and IgA-lambda monoclonal gammopathy of underdetermined significance.We believe that this is one of the rare cases consistent with the recently described TEMPI syndrome.

View Article: PubMed Central - PubMed

Affiliation: Division of Nephrology, Department of Internal Medicine , Saint Louis University Health Science Center , Saint Louis, MO , USA.

ABSTRACT
We present an interesting case of a woman with new onset hypertension and abdominal fullness who was found to have huge bilateral perinephric fluid collections. Extensive workup revealed that she had secondary polycythemia, extensive truncal and proximal extremities telangiectasia and IgA-lambda monoclonal gammopathy of underdetermined significance. We believe that this is one of the rare cases consistent with the recently described TEMPI syndrome.

No MeSH data available.


Related in: MedlinePlus

CT scan of abdomen shows multiple perinephric cystic fluid collections compressing both the kidneys.
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SFS139F1: CT scan of abdomen shows multiple perinephric cystic fluid collections compressing both the kidneys.

Mentions: A 58-year-old woman was referred to our clinic for evaluation of uncontrolled hypertension and fluid collections surrounding the kidneys bilaterally. The patient had been doing well until ∼6 months prior to presentation, when she developed indigestion and bloating. She was diagnosed with worsening hypertension over the past 2–3 years. An ultrasound of the abdomen 2 months prior to presentation showed large cystic structures surrounding both the kidneys, dilation of common bile duct (1.2 cm), liver hemangioma and also non-obstructing gallstones. A computed tomography (CT) scan of the abdomen and pelvis revealed bilateral perinephric fluid collections compressing both the kidneys (Figure 1). The renal parenchyma appeared normal. There was also right hydronephrosis and proximal hydroureter along with enhanced liver lesions, most likely hemangiomas. There was mild extrahepatic biliary duct dilatation and colonic diverticulosis.Fig. 1.


A new case of TEMPI syndrome.

Mohammadi F, Wolverson MK, Bastani B - Clin Kidney J (2012)

CT scan of abdomen shows multiple perinephric cystic fluid collections compressing both the kidneys.
© Copyright Policy - creative-commons
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC4400562&req=5

SFS139F1: CT scan of abdomen shows multiple perinephric cystic fluid collections compressing both the kidneys.
Mentions: A 58-year-old woman was referred to our clinic for evaluation of uncontrolled hypertension and fluid collections surrounding the kidneys bilaterally. The patient had been doing well until ∼6 months prior to presentation, when she developed indigestion and bloating. She was diagnosed with worsening hypertension over the past 2–3 years. An ultrasound of the abdomen 2 months prior to presentation showed large cystic structures surrounding both the kidneys, dilation of common bile duct (1.2 cm), liver hemangioma and also non-obstructing gallstones. A computed tomography (CT) scan of the abdomen and pelvis revealed bilateral perinephric fluid collections compressing both the kidneys (Figure 1). The renal parenchyma appeared normal. There was also right hydronephrosis and proximal hydroureter along with enhanced liver lesions, most likely hemangiomas. There was mild extrahepatic biliary duct dilatation and colonic diverticulosis.Fig. 1.

Bottom Line: We present an interesting case of a woman with new onset hypertension and abdominal fullness who was found to have huge bilateral perinephric fluid collections.Extensive workup revealed that she had secondary polycythemia, extensive truncal and proximal extremities telangiectasia and IgA-lambda monoclonal gammopathy of underdetermined significance.We believe that this is one of the rare cases consistent with the recently described TEMPI syndrome.

View Article: PubMed Central - PubMed

Affiliation: Division of Nephrology, Department of Internal Medicine , Saint Louis University Health Science Center , Saint Louis, MO , USA.

ABSTRACT
We present an interesting case of a woman with new onset hypertension and abdominal fullness who was found to have huge bilateral perinephric fluid collections. Extensive workup revealed that she had secondary polycythemia, extensive truncal and proximal extremities telangiectasia and IgA-lambda monoclonal gammopathy of underdetermined significance. We believe that this is one of the rare cases consistent with the recently described TEMPI syndrome.

No MeSH data available.


Related in: MedlinePlus