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Congenital milia en plaque on scalp.

Ghosh S, Sangal S - Indian J Dermatol (2015 Jan-Feb)

Bottom Line: Fewer than 40 cases have been reported so far in dermatological literature, and most cases are described to occur in adults and in the peri-auricular area.We describe a case of congenital MEP on scalp of a five-year-old boy with a blaschkoid extension into posterior nuchal area.This case report claims its uniqueness because of the unusual site and congenital presentation.

View Article: PubMed Central - PubMed

Affiliation: Departments of Skin and VD, and PGIMS, Rohtak, Haryana, India.

ABSTRACT
Milia en plaque is a rare disease entity characterized by confluence of multiple keratin-filled cysts resulting from the obstruction of hair follicle without any preceding primary dermatosis. Fewer than 40 cases have been reported so far in dermatological literature, and most cases are described to occur in adults and in the peri-auricular area. We describe a case of congenital MEP on scalp of a five-year-old boy with a blaschkoid extension into posterior nuchal area. This case report claims its uniqueness because of the unusual site and congenital presentation.

No MeSH data available.


Related in: MedlinePlus

(a) Irregular, circumscribed erythematous, infiltrated plaque with complete alopecia and an uneven surface studded with multiple whitish globoid structures, on the left parietal scalp of a 5-year-old boy, (b) Same plaque showing a marginal extension of milia in a linear fashion along the posterior nuchal area following blaschkoid patten
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Figure 1: (a) Irregular, circumscribed erythematous, infiltrated plaque with complete alopecia and an uneven surface studded with multiple whitish globoid structures, on the left parietal scalp of a 5-year-old boy, (b) Same plaque showing a marginal extension of milia in a linear fashion along the posterior nuchal area following blaschkoid patten

Mentions: On examination, there was 5 × 6 cm2 irregular, circumscribed erythematous and edematous plaque on the left parietal scalp, 6 cm above the mastoid tubercle. The surface of the plaque was devoid of hair and studded with multiple white milia of variable sizes [Figure 1a]. On needling one of the intact milia, white thick material was extruded from it, which was determined to be sterile after performing Gram stain. On palpation, there was no tenderness, induration, or increase in temperature. There were no comedones or any pustules or pus exudation on applying pressure over and around the lesion. There were areas of scarring and superficial crusting in few areas of the plaque. From the lower margin of the plaque, few discrete minute milia spread beyond the inferior margin of the original lesion, to be distributed in a linear fashion, extending up to the posterior nuchal area following a Blaschkoid pattern [Figure 1b]. However, bilateral retroauricular areas were spared of any milia. Potassium hydroxide (KOH) mount of hair uprooted from the margin of plaque did not reveal any fungal element.


Congenital milia en plaque on scalp.

Ghosh S, Sangal S - Indian J Dermatol (2015 Jan-Feb)

(a) Irregular, circumscribed erythematous, infiltrated plaque with complete alopecia and an uneven surface studded with multiple whitish globoid structures, on the left parietal scalp of a 5-year-old boy, (b) Same plaque showing a marginal extension of milia in a linear fashion along the posterior nuchal area following blaschkoid patten
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC4318039&req=5

Figure 1: (a) Irregular, circumscribed erythematous, infiltrated plaque with complete alopecia and an uneven surface studded with multiple whitish globoid structures, on the left parietal scalp of a 5-year-old boy, (b) Same plaque showing a marginal extension of milia in a linear fashion along the posterior nuchal area following blaschkoid patten
Mentions: On examination, there was 5 × 6 cm2 irregular, circumscribed erythematous and edematous plaque on the left parietal scalp, 6 cm above the mastoid tubercle. The surface of the plaque was devoid of hair and studded with multiple white milia of variable sizes [Figure 1a]. On needling one of the intact milia, white thick material was extruded from it, which was determined to be sterile after performing Gram stain. On palpation, there was no tenderness, induration, or increase in temperature. There were no comedones or any pustules or pus exudation on applying pressure over and around the lesion. There were areas of scarring and superficial crusting in few areas of the plaque. From the lower margin of the plaque, few discrete minute milia spread beyond the inferior margin of the original lesion, to be distributed in a linear fashion, extending up to the posterior nuchal area following a Blaschkoid pattern [Figure 1b]. However, bilateral retroauricular areas were spared of any milia. Potassium hydroxide (KOH) mount of hair uprooted from the margin of plaque did not reveal any fungal element.

Bottom Line: Fewer than 40 cases have been reported so far in dermatological literature, and most cases are described to occur in adults and in the peri-auricular area.We describe a case of congenital MEP on scalp of a five-year-old boy with a blaschkoid extension into posterior nuchal area.This case report claims its uniqueness because of the unusual site and congenital presentation.

View Article: PubMed Central - PubMed

Affiliation: Departments of Skin and VD, and PGIMS, Rohtak, Haryana, India.

ABSTRACT
Milia en plaque is a rare disease entity characterized by confluence of multiple keratin-filled cysts resulting from the obstruction of hair follicle without any preceding primary dermatosis. Fewer than 40 cases have been reported so far in dermatological literature, and most cases are described to occur in adults and in the peri-auricular area. We describe a case of congenital MEP on scalp of a five-year-old boy with a blaschkoid extension into posterior nuchal area. This case report claims its uniqueness because of the unusual site and congenital presentation.

No MeSH data available.


Related in: MedlinePlus