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Immature teratoma at umbilicus region presenting as exomphalos: A case report with review of literature.

Chavali LV, Bhaskar RV, Reddy JB - Indian J Med Paediatr Oncol (2014)

Bottom Line: Umbilical cord neoplasms are rare.Teratomas, which are accepted as the only true neoplasms at this site, are exceptional.Immature elements as seen in our case are rare.

View Article: PubMed Central - PubMed

Affiliation: Department of Pathology, Rangaraya Medical College, Kakinada, Andhra Pradesh, India.

ABSTRACT
Umbilical cord neoplasms are rare. Teratomas, which are accepted as the only true neoplasms at this site, are exceptional. These tumors are polymorphic in their presentation and are often associated with other abnormalities, with exomphalos being the most common abnormality. Histologically these tumors show mature tissues from all the three-germ layers. Immature elements as seen in our case are rare. Germ cells which have gone astray during embryonic development are thought to be the cells of origin of these tumors.

No MeSH data available.


Related in: MedlinePlus

Clinical photograph at presentation
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Figure 1: Clinical photograph at presentation

Mentions: The neonate was sent to a tertiary care hospital for specialist care on the 2nd day, wherein she developed bilious vomiting. Suspecting intestinal obstruction, emergency surgery was done. The surgeon found a partly skin covered nodular mass protruding from the anterior abdominal wall with the umbilical cord lateral to it, along with a normal segment of small bowel protruding out. Prominent veins were seen coursing over the anterior abdominal wall above the mass [Figure 1]. Intraoperatively the mass was found to contain nodules of adipose tissue covered over by skin with a peau de orange appearance along with firm gritty areas. It could be shelled out easily with attachment only at the umbilical ring. Duodenal atresia beyond the level of opening of the bile duct was noted intra-abdominally. A duodeno-duodenal anastamoses was done and the resected mass was sent for histopathological examination with a diagnosis of a teratoma. The neonate expired on the 2nd postoperative day due to hypothermia and sepsis.


Immature teratoma at umbilicus region presenting as exomphalos: A case report with review of literature.

Chavali LV, Bhaskar RV, Reddy JB - Indian J Med Paediatr Oncol (2014)

Clinical photograph at presentation
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC4202622&req=5

Figure 1: Clinical photograph at presentation
Mentions: The neonate was sent to a tertiary care hospital for specialist care on the 2nd day, wherein she developed bilious vomiting. Suspecting intestinal obstruction, emergency surgery was done. The surgeon found a partly skin covered nodular mass protruding from the anterior abdominal wall with the umbilical cord lateral to it, along with a normal segment of small bowel protruding out. Prominent veins were seen coursing over the anterior abdominal wall above the mass [Figure 1]. Intraoperatively the mass was found to contain nodules of adipose tissue covered over by skin with a peau de orange appearance along with firm gritty areas. It could be shelled out easily with attachment only at the umbilical ring. Duodenal atresia beyond the level of opening of the bile duct was noted intra-abdominally. A duodeno-duodenal anastamoses was done and the resected mass was sent for histopathological examination with a diagnosis of a teratoma. The neonate expired on the 2nd postoperative day due to hypothermia and sepsis.

Bottom Line: Umbilical cord neoplasms are rare.Teratomas, which are accepted as the only true neoplasms at this site, are exceptional.Immature elements as seen in our case are rare.

View Article: PubMed Central - PubMed

Affiliation: Department of Pathology, Rangaraya Medical College, Kakinada, Andhra Pradesh, India.

ABSTRACT
Umbilical cord neoplasms are rare. Teratomas, which are accepted as the only true neoplasms at this site, are exceptional. These tumors are polymorphic in their presentation and are often associated with other abnormalities, with exomphalos being the most common abnormality. Histologically these tumors show mature tissues from all the three-germ layers. Immature elements as seen in our case are rare. Germ cells which have gone astray during embryonic development are thought to be the cells of origin of these tumors.

No MeSH data available.


Related in: MedlinePlus