Limits...
Functioning endometrium and endometrioma in a patient with mayer-rokitanski-kuster-hauser syndrome.

Kawano Y, Hirakawa T, Nishida M, Yuge A, Yano M, Nasu K, Narahara H - Jpn Clin Med (2014)

Bottom Line: Mayer-Rokitanski-Kuster-Hauser (MRKH) syndrome is a rare disease.A 27-year-old woman was admitted for primary amenorrhea and cyclic pelvic pain.Accurate evaluation before the operation and informed consent are necessary to treat patients with MRKH syndrome.

View Article: PubMed Central - PubMed

Affiliation: Department of Obstetrics and Gynecology, Faculty of Medicine, Oita University, Yufu, Oita, Japan.

ABSTRACT
Mayer-Rokitanski-Kuster-Hauser (MRKH) syndrome is a rare disease. A 27-year-old woman was admitted for primary amenorrhea and cyclic pelvic pain. Magnetic resonance imaging (MRI) revealed bilateral Müllerian remnants with functioning endometrium and a pelvic mass considered to be an endometriotic cyst. Bilateral Müllerian remnants were removed, and right ovarian cystectomy was performed at laparoscopic surgery. Accurate evaluation before the operation and informed consent are necessary to treat patients with MRKH syndrome.

No MeSH data available.


Related in: MedlinePlus

Pathological analysis of the endometriotic lesion in the right ovary (A: hemosiderin deposit site, H&E, ×10) and endometrial tissues in bilateral uterine horns (B,C: H&E, ×10).
© Copyright Policy - open-access
Related In: Results  -  Collection


getmorefigures.php?uid=PMC4196889&req=5

f3-jcm-5-2014-043: Pathological analysis of the endometriotic lesion in the right ovary (A: hemosiderin deposit site, H&E, ×10) and endometrial tissues in bilateral uterine horns (B,C: H&E, ×10).

Mentions: Laparoscopic surgery to remove the abnormal structures was planned. After the patients gave written informed consent, vaginoplasty with a vaginal dilator (Protese, Atom Medical Co Ltd, Tokyo, Japan) was performed. The patient also underwent laparoscopic cystectomy of the right ovarian endometriotic cyst and resection of the Müllerian remnants. Bilateral fibrous bands with uterine horns were also removed, whereas the left ovary and fallopian tube were left in situ (Fig. 2). The findings of the operative specimen revealed a non-canalized bilateral uterine horn with functional small endometrium, thinning smooth muscle, fibrotic right ovary, and, under histopathologic examination an endometriotic cyst (Fig. 3).


Functioning endometrium and endometrioma in a patient with mayer-rokitanski-kuster-hauser syndrome.

Kawano Y, Hirakawa T, Nishida M, Yuge A, Yano M, Nasu K, Narahara H - Jpn Clin Med (2014)

Pathological analysis of the endometriotic lesion in the right ovary (A: hemosiderin deposit site, H&E, ×10) and endometrial tissues in bilateral uterine horns (B,C: H&E, ×10).
© Copyright Policy - open-access
Related In: Results  -  Collection

Show All Figures
getmorefigures.php?uid=PMC4196889&req=5

f3-jcm-5-2014-043: Pathological analysis of the endometriotic lesion in the right ovary (A: hemosiderin deposit site, H&E, ×10) and endometrial tissues in bilateral uterine horns (B,C: H&E, ×10).
Mentions: Laparoscopic surgery to remove the abnormal structures was planned. After the patients gave written informed consent, vaginoplasty with a vaginal dilator (Protese, Atom Medical Co Ltd, Tokyo, Japan) was performed. The patient also underwent laparoscopic cystectomy of the right ovarian endometriotic cyst and resection of the Müllerian remnants. Bilateral fibrous bands with uterine horns were also removed, whereas the left ovary and fallopian tube were left in situ (Fig. 2). The findings of the operative specimen revealed a non-canalized bilateral uterine horn with functional small endometrium, thinning smooth muscle, fibrotic right ovary, and, under histopathologic examination an endometriotic cyst (Fig. 3).

Bottom Line: Mayer-Rokitanski-Kuster-Hauser (MRKH) syndrome is a rare disease.A 27-year-old woman was admitted for primary amenorrhea and cyclic pelvic pain.Accurate evaluation before the operation and informed consent are necessary to treat patients with MRKH syndrome.

View Article: PubMed Central - PubMed

Affiliation: Department of Obstetrics and Gynecology, Faculty of Medicine, Oita University, Yufu, Oita, Japan.

ABSTRACT
Mayer-Rokitanski-Kuster-Hauser (MRKH) syndrome is a rare disease. A 27-year-old woman was admitted for primary amenorrhea and cyclic pelvic pain. Magnetic resonance imaging (MRI) revealed bilateral Müllerian remnants with functioning endometrium and a pelvic mass considered to be an endometriotic cyst. Bilateral Müllerian remnants were removed, and right ovarian cystectomy was performed at laparoscopic surgery. Accurate evaluation before the operation and informed consent are necessary to treat patients with MRKH syndrome.

No MeSH data available.


Related in: MedlinePlus