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Cases of atypical lymphangiomas in children.

Minocha PK, Roop L, Persad R - Case Rep Pediatr (2014)

Bottom Line: They are most frequently found in the neck and axilla, while intra-abdominal and mediastinal lymphangiomas are uncommon.Conclusion.We believe that ultrasound scan is very good at detection of the lesion, while CT is better at determining tumour content and planning for the operation.

View Article: PubMed Central - PubMed

Affiliation: Department of Paediatric Surgery, San Fernando General Hospital, Trinidad, Trinidad and Tobago.

ABSTRACT
Background. Lymphatic malformations or lymphangiomas are rare benign hamartomas that result from maldevelopment of primitive lymphatic sacs. They are most frequently found in the neck and axilla, while intra-abdominal and mediastinal lymphangiomas are uncommon. These are primarily tumours of infancy and childhood and are successfully treated with surgical excision. Summary of Cases. Five cases of lymphangioma comprising three intra-abdominal lymphangiomas and two unilateral axillary lymphangiomas presenting at one institution in Trinidad W.I. between 2005 and 2012 were examined. The presentations, location, workup, treatment, and outcome of these patients were studied. Conclusion. This paper discusses a range of extracervical lymphangioma cases seen at San Fernando General Hospital, Trinidad W.I. We report three intra-abdominal cases and the most common clinical presentations were abdominal pain and distension. Also two axillary cases were reported, which presented as painless axillary masses. The major concerns for excision of axillary lymphangioma by parents and surgeons were cosmesis and feasibility of complete resection without disruption of developing breast tissue and axillary vessels. We believe that ultrasound scan is very good at detection of the lesion, while CT is better at determining tumour content and planning for the operation. It is our opinion that complete surgical excision can be achieved.

No MeSH data available.


Related in: MedlinePlus

Abdominal CT showing a 13 cm × 8 cm × 12 cm cystic abdominal mass.
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fig3: Abdominal CT showing a 13 cm × 8 cm × 12 cm cystic abdominal mass.

Mentions: The patient was a 4-year-old female who was referred from a rural health center with 2-week history of progressive abdominal distension. She was otherwise asymptomatic with a positive history of passing stool and flatus. There was no significant past medical history or history of prior abdominal surgery or trauma. She had no family history of malignancy or congenital abnormalities. On abdominal examination, a mass arising from the pelvis was palpable. An abdominal USS revealed a 14 cm by 7 cm by 12 cm fluid filled structure in the left half of the abdomen extending into the pelvic cavity (Figure 2). Abdominal CT with IV contrast showed a 13 cm by 8 cm by 12 cm cystic abdominal mass that appeared to arise from the pelvis extending into the abdomen and displacing the bowel bilaterally (Figure 3). Two days subsequent to admission, the patient had exploratory laparotomy and cystectomy. A 15 cm by 12 cm mesenteric cyst containing chocolate coloured fluid was found at the splenic hilum surrounded by a jejunal loop and bordered by the tail of the pancreas. She had uneventful recovery with no evidence of recurrence to date. Histology showed a mixture of lymph vessels and smooth muscle, features suggestive of lymphangioma (Figure 4).


Cases of atypical lymphangiomas in children.

Minocha PK, Roop L, Persad R - Case Rep Pediatr (2014)

Abdominal CT showing a 13 cm × 8 cm × 12 cm cystic abdominal mass.
© Copyright Policy - open-access
Related In: Results  -  Collection

Show All Figures
getmorefigures.php?uid=PMC4195264&req=5

fig3: Abdominal CT showing a 13 cm × 8 cm × 12 cm cystic abdominal mass.
Mentions: The patient was a 4-year-old female who was referred from a rural health center with 2-week history of progressive abdominal distension. She was otherwise asymptomatic with a positive history of passing stool and flatus. There was no significant past medical history or history of prior abdominal surgery or trauma. She had no family history of malignancy or congenital abnormalities. On abdominal examination, a mass arising from the pelvis was palpable. An abdominal USS revealed a 14 cm by 7 cm by 12 cm fluid filled structure in the left half of the abdomen extending into the pelvic cavity (Figure 2). Abdominal CT with IV contrast showed a 13 cm by 8 cm by 12 cm cystic abdominal mass that appeared to arise from the pelvis extending into the abdomen and displacing the bowel bilaterally (Figure 3). Two days subsequent to admission, the patient had exploratory laparotomy and cystectomy. A 15 cm by 12 cm mesenteric cyst containing chocolate coloured fluid was found at the splenic hilum surrounded by a jejunal loop and bordered by the tail of the pancreas. She had uneventful recovery with no evidence of recurrence to date. Histology showed a mixture of lymph vessels and smooth muscle, features suggestive of lymphangioma (Figure 4).

Bottom Line: They are most frequently found in the neck and axilla, while intra-abdominal and mediastinal lymphangiomas are uncommon.Conclusion.We believe that ultrasound scan is very good at detection of the lesion, while CT is better at determining tumour content and planning for the operation.

View Article: PubMed Central - PubMed

Affiliation: Department of Paediatric Surgery, San Fernando General Hospital, Trinidad, Trinidad and Tobago.

ABSTRACT
Background. Lymphatic malformations or lymphangiomas are rare benign hamartomas that result from maldevelopment of primitive lymphatic sacs. They are most frequently found in the neck and axilla, while intra-abdominal and mediastinal lymphangiomas are uncommon. These are primarily tumours of infancy and childhood and are successfully treated with surgical excision. Summary of Cases. Five cases of lymphangioma comprising three intra-abdominal lymphangiomas and two unilateral axillary lymphangiomas presenting at one institution in Trinidad W.I. between 2005 and 2012 were examined. The presentations, location, workup, treatment, and outcome of these patients were studied. Conclusion. This paper discusses a range of extracervical lymphangioma cases seen at San Fernando General Hospital, Trinidad W.I. We report three intra-abdominal cases and the most common clinical presentations were abdominal pain and distension. Also two axillary cases were reported, which presented as painless axillary masses. The major concerns for excision of axillary lymphangioma by parents and surgeons were cosmesis and feasibility of complete resection without disruption of developing breast tissue and axillary vessels. We believe that ultrasound scan is very good at detection of the lesion, while CT is better at determining tumour content and planning for the operation. It is our opinion that complete surgical excision can be achieved.

No MeSH data available.


Related in: MedlinePlus