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Cases of atypical lymphangiomas in children.

Minocha PK, Roop L, Persad R - Case Rep Pediatr (2014)

Bottom Line: They are most frequently found in the neck and axilla, while intra-abdominal and mediastinal lymphangiomas are uncommon.Conclusion.We believe that ultrasound scan is very good at detection of the lesion, while CT is better at determining tumour content and planning for the operation.

View Article: PubMed Central - PubMed

Affiliation: Department of Paediatric Surgery, San Fernando General Hospital, Trinidad, Trinidad and Tobago.

ABSTRACT
Background. Lymphatic malformations or lymphangiomas are rare benign hamartomas that result from maldevelopment of primitive lymphatic sacs. They are most frequently found in the neck and axilla, while intra-abdominal and mediastinal lymphangiomas are uncommon. These are primarily tumours of infancy and childhood and are successfully treated with surgical excision. Summary of Cases. Five cases of lymphangioma comprising three intra-abdominal lymphangiomas and two unilateral axillary lymphangiomas presenting at one institution in Trinidad W.I. between 2005 and 2012 were examined. The presentations, location, workup, treatment, and outcome of these patients were studied. Conclusion. This paper discusses a range of extracervical lymphangioma cases seen at San Fernando General Hospital, Trinidad W.I. We report three intra-abdominal cases and the most common clinical presentations were abdominal pain and distension. Also two axillary cases were reported, which presented as painless axillary masses. The major concerns for excision of axillary lymphangioma by parents and surgeons were cosmesis and feasibility of complete resection without disruption of developing breast tissue and axillary vessels. We believe that ultrasound scan is very good at detection of the lesion, while CT is better at determining tumour content and planning for the operation. It is our opinion that complete surgical excision can be achieved.

No MeSH data available.


Related in: MedlinePlus

CT of the abdomen showing a 30 cm × 10 cm left sided isodense retroperitoneal mass.
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Related In: Results  -  Collection


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fig1: CT of the abdomen showing a 30 cm × 10 cm left sided isodense retroperitoneal mass.

Mentions: A 4-year-old male presented with 2-day history of periumbilical pain and a past history of occasional constipation without any significant past medical history and no family history of malignancy or congenital abnormalities. On examination he was found to have a mildly distended, nontender abdomen with diffuse left flank firmness, but no discrete mass was appreciated. The patient continued to have colicky abdominal pain but no constipation or vomiting. CT scan abdomen with IV contrast was performed which showed a 30 cm by 10 cm left sided isodense retroperitoneal mass attached to the lower pole of left kidney (Figure 1). Based on imaging, the possible differential diagnoses included neuroblastoma and cystic lymphangioma. The patient underwent an exploratory laparotomy which revealed a 20 cm by 30 cm multiloculated cystic mass arising retroperitoneally from the coeliac plexus of lymph. The hilum of the cyst was anterior to splenic artery displacing pancreas laterally to the right. The histology of the specimen confirmed intra-abdominal cystic lymphangioma. Yearly follow-up with USS for the past 8 years has shown no recurrence thus far.


Cases of atypical lymphangiomas in children.

Minocha PK, Roop L, Persad R - Case Rep Pediatr (2014)

CT of the abdomen showing a 30 cm × 10 cm left sided isodense retroperitoneal mass.
© Copyright Policy - open-access
Related In: Results  -  Collection

Show All Figures
getmorefigures.php?uid=PMC4195264&req=5

fig1: CT of the abdomen showing a 30 cm × 10 cm left sided isodense retroperitoneal mass.
Mentions: A 4-year-old male presented with 2-day history of periumbilical pain and a past history of occasional constipation without any significant past medical history and no family history of malignancy or congenital abnormalities. On examination he was found to have a mildly distended, nontender abdomen with diffuse left flank firmness, but no discrete mass was appreciated. The patient continued to have colicky abdominal pain but no constipation or vomiting. CT scan abdomen with IV contrast was performed which showed a 30 cm by 10 cm left sided isodense retroperitoneal mass attached to the lower pole of left kidney (Figure 1). Based on imaging, the possible differential diagnoses included neuroblastoma and cystic lymphangioma. The patient underwent an exploratory laparotomy which revealed a 20 cm by 30 cm multiloculated cystic mass arising retroperitoneally from the coeliac plexus of lymph. The hilum of the cyst was anterior to splenic artery displacing pancreas laterally to the right. The histology of the specimen confirmed intra-abdominal cystic lymphangioma. Yearly follow-up with USS for the past 8 years has shown no recurrence thus far.

Bottom Line: They are most frequently found in the neck and axilla, while intra-abdominal and mediastinal lymphangiomas are uncommon.Conclusion.We believe that ultrasound scan is very good at detection of the lesion, while CT is better at determining tumour content and planning for the operation.

View Article: PubMed Central - PubMed

Affiliation: Department of Paediatric Surgery, San Fernando General Hospital, Trinidad, Trinidad and Tobago.

ABSTRACT
Background. Lymphatic malformations or lymphangiomas are rare benign hamartomas that result from maldevelopment of primitive lymphatic sacs. They are most frequently found in the neck and axilla, while intra-abdominal and mediastinal lymphangiomas are uncommon. These are primarily tumours of infancy and childhood and are successfully treated with surgical excision. Summary of Cases. Five cases of lymphangioma comprising three intra-abdominal lymphangiomas and two unilateral axillary lymphangiomas presenting at one institution in Trinidad W.I. between 2005 and 2012 were examined. The presentations, location, workup, treatment, and outcome of these patients were studied. Conclusion. This paper discusses a range of extracervical lymphangioma cases seen at San Fernando General Hospital, Trinidad W.I. We report three intra-abdominal cases and the most common clinical presentations were abdominal pain and distension. Also two axillary cases were reported, which presented as painless axillary masses. The major concerns for excision of axillary lymphangioma by parents and surgeons were cosmesis and feasibility of complete resection without disruption of developing breast tissue and axillary vessels. We believe that ultrasound scan is very good at detection of the lesion, while CT is better at determining tumour content and planning for the operation. It is our opinion that complete surgical excision can be achieved.

No MeSH data available.


Related in: MedlinePlus