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Complete androgen insensitivity syndrome with a large gonadal serous papillary cystadenofibroma.

Ozdemir O, Sari ME, Akmut E, Selimova V, Unal T, Atalay CR - J Hum Reprod Sci (2014)

Bottom Line: We performed bilateral gonadectomy.The pathology showed testicular tissue in the right inguinal mass and a serous papillary cystadenofibroma in the left one.Gonadectomy should be performed right after puberty to prevent the risk of malignancy development in the testes.

View Article: PubMed Central - PubMed

Affiliation: Department of Gynecology and Obstetrics, Ankara Numune Education and Research Hospital, Ankara, Turkey.

ABSTRACT
We present a patient with complete androgen insensitivity syndrome (CAIS) diagnosed with a serous papillary cystadenofibroma. A 41-year-old married female with a mass in the left inguinal region and a history of primary amenorrhea. A bulging mass of 13.7 cm × 8 cm × 12.4 cm in the left inguinal region extending from the hip joint to the level of labia majus, and a 3.2 cm × 2.8 cm mass in her right inguinal region were found by ultrasonography and magnetic resonance imaging. We performed bilateral gonadectomy. The pathology showed testicular tissue in the right inguinal mass and a serous papillary cystadenofibroma in the left one. CAIS is an infrequent clinical entity, occurrence of serous papillary cystadenofibroma is even rarer in this syndrome serous cystadenofibroma should come to mind in patients with a huge inguinal mass. Gonadectomy should be performed right after puberty to prevent the risk of malignancy development in the testes.

No MeSH data available.


Related in: MedlinePlus

Microscopic appearance of the right gonad (H and E, ×10)
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Figure 2: Microscopic appearance of the right gonad (H and E, ×10)

Mentions: Histopathologic examination revealed immature seminiferous tubules surrounded by immature germ cells and sertoli cells in the mass from the right inguinal region, and a serous papillary cystadenofibroma in the one from the left. No signs of spermatogenesis or leydig cell hyperplasia in the interstitial tissue were seen in both gonads [Figures 2-4]. Estrogen therapy was initiated postoperatively.


Complete androgen insensitivity syndrome with a large gonadal serous papillary cystadenofibroma.

Ozdemir O, Sari ME, Akmut E, Selimova V, Unal T, Atalay CR - J Hum Reprod Sci (2014)

Microscopic appearance of the right gonad (H and E, ×10)
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC4150143&req=5

Figure 2: Microscopic appearance of the right gonad (H and E, ×10)
Mentions: Histopathologic examination revealed immature seminiferous tubules surrounded by immature germ cells and sertoli cells in the mass from the right inguinal region, and a serous papillary cystadenofibroma in the one from the left. No signs of spermatogenesis or leydig cell hyperplasia in the interstitial tissue were seen in both gonads [Figures 2-4]. Estrogen therapy was initiated postoperatively.

Bottom Line: We performed bilateral gonadectomy.The pathology showed testicular tissue in the right inguinal mass and a serous papillary cystadenofibroma in the left one.Gonadectomy should be performed right after puberty to prevent the risk of malignancy development in the testes.

View Article: PubMed Central - PubMed

Affiliation: Department of Gynecology and Obstetrics, Ankara Numune Education and Research Hospital, Ankara, Turkey.

ABSTRACT
We present a patient with complete androgen insensitivity syndrome (CAIS) diagnosed with a serous papillary cystadenofibroma. A 41-year-old married female with a mass in the left inguinal region and a history of primary amenorrhea. A bulging mass of 13.7 cm × 8 cm × 12.4 cm in the left inguinal region extending from the hip joint to the level of labia majus, and a 3.2 cm × 2.8 cm mass in her right inguinal region were found by ultrasonography and magnetic resonance imaging. We performed bilateral gonadectomy. The pathology showed testicular tissue in the right inguinal mass and a serous papillary cystadenofibroma in the left one. CAIS is an infrequent clinical entity, occurrence of serous papillary cystadenofibroma is even rarer in this syndrome serous cystadenofibroma should come to mind in patients with a huge inguinal mass. Gonadectomy should be performed right after puberty to prevent the risk of malignancy development in the testes.

No MeSH data available.


Related in: MedlinePlus