Limits...
Unilateral pulmonary agenesis.

Jentzsch NS - J Bras Pneumol (2014 May-Jun)

View Article: PubMed Central - PubMed

Affiliation: Minas Gerais School of Medical Sciences, São José University Hospital, Belo Horizonte, Brazil.

AUTOMATICALLY GENERATED EXCERPT
Please rate it.

unilateral pulmonary agenesis in an 8-year-old asymptomatic male child without other After 48 days of gestation, the segmental and subsegmental bronchi start The mortality rate is higher when there is agenesis of the right lung... difference can be explained by a greater mediastinal shift, leading to tracheal compression... remaining lung and its herniation into the contralateral hemithorax... Asymptomatic patients do not require intervention, especially in the absence of associated anomalies... delayed, being made in adulthood in asymptomatic patients... Other associated malformations The prognosis is better when there is agenesis of the left lung and when there are no cardiac malformations.

Show MeSH

Related in: MedlinePlus

Chest CT scans showing absence of the left lung.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
getmorefigures.php?uid=PMC4109206&req=5

f02: Chest CT scans showing absence of the left lung.

Mentions: I would like to report that we treated a 3-month-old female infant, from the city of BeloHorizonte, Brazil, who had been born at term and had undergone prenatal testinguneventfully. The infant was taken to the Department of Pediatrics of the São JoséUniversity Hospital in that same city on March of 2012 with a 4-day-history of cough andfever. Her parents reported that she had no comorbidities or previous hospitalizations. Thepatient presented with acute respiratory failure and required oxygen by nasal catheter.Examination of the respiratory system revealed diminished breath sounds throughout the lefthemithorax, without adventitious sounds. A chest X-ray (Figure 1) showed complete opacification of the left hemithorax, together withdeviation of the trachea and mediastinum to the left. The left lung was not seen on chestCT (Figure 2). Doppler echocardiography showedagenesis of the left pulmonary artery, without other cardiac abnormalities, andbronchoscopy revealed complete absence of the left lung and absence of bronchial stump. Adiagnosis of left lung agenesis was therefore established. The patient's course wassatisfactory, and she is under outpatient follow-up. Congenital malformations of the lungare rare and vary widely in their clinical presentation and severity, depending mostly onthe degree of lung involvement and their location in the thoracic cavity.(2) The earliest stage of lung development occurs during the first 50 days ofgestation and is called embryonic stage: around the 26th day, the anterior part of theforegut invaginates and forms the laryngotracheal bud; subsequently, the two main bronchiare formed. After 48 days of gestation, the segmental and subsegmental bronchi startforming. The pulmonary arteries form from the sixth aortic arch, and the pulmonary veinsform from the invagination of the sinoatrial region of the heart. The development of theconducting airways starts early, whereas the respiratory bronchioles, alveolar ducts, andalveoli form later in gestation, in the stages called pseudoglandular, canalicular,saccular, and alveolar.


Unilateral pulmonary agenesis.

Jentzsch NS - J Bras Pneumol (2014 May-Jun)

Chest CT scans showing absence of the left lung.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC4109206&req=5

f02: Chest CT scans showing absence of the left lung.
Mentions: I would like to report that we treated a 3-month-old female infant, from the city of BeloHorizonte, Brazil, who had been born at term and had undergone prenatal testinguneventfully. The infant was taken to the Department of Pediatrics of the São JoséUniversity Hospital in that same city on March of 2012 with a 4-day-history of cough andfever. Her parents reported that she had no comorbidities or previous hospitalizations. Thepatient presented with acute respiratory failure and required oxygen by nasal catheter.Examination of the respiratory system revealed diminished breath sounds throughout the lefthemithorax, without adventitious sounds. A chest X-ray (Figure 1) showed complete opacification of the left hemithorax, together withdeviation of the trachea and mediastinum to the left. The left lung was not seen on chestCT (Figure 2). Doppler echocardiography showedagenesis of the left pulmonary artery, without other cardiac abnormalities, andbronchoscopy revealed complete absence of the left lung and absence of bronchial stump. Adiagnosis of left lung agenesis was therefore established. The patient's course wassatisfactory, and she is under outpatient follow-up. Congenital malformations of the lungare rare and vary widely in their clinical presentation and severity, depending mostly onthe degree of lung involvement and their location in the thoracic cavity.(2) The earliest stage of lung development occurs during the first 50 days ofgestation and is called embryonic stage: around the 26th day, the anterior part of theforegut invaginates and forms the laryngotracheal bud; subsequently, the two main bronchiare formed. After 48 days of gestation, the segmental and subsegmental bronchi startforming. The pulmonary arteries form from the sixth aortic arch, and the pulmonary veinsform from the invagination of the sinoatrial region of the heart. The development of theconducting airways starts early, whereas the respiratory bronchioles, alveolar ducts, andalveoli form later in gestation, in the stages called pseudoglandular, canalicular,saccular, and alveolar.

View Article: PubMed Central - PubMed

Affiliation: Minas Gerais School of Medical Sciences, São José University Hospital, Belo Horizonte, Brazil.

AUTOMATICALLY GENERATED EXCERPT
Please rate it.

unilateral pulmonary agenesis in an 8-year-old asymptomatic male child without other After 48 days of gestation, the segmental and subsegmental bronchi start The mortality rate is higher when there is agenesis of the right lung... difference can be explained by a greater mediastinal shift, leading to tracheal compression... remaining lung and its herniation into the contralateral hemithorax... Asymptomatic patients do not require intervention, especially in the absence of associated anomalies... delayed, being made in adulthood in asymptomatic patients... Other associated malformations The prognosis is better when there is agenesis of the left lung and when there are no cardiac malformations.

Show MeSH
Related in: MedlinePlus