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Sprengel deformity and Klippel-Feil syndrome leading to cervical myelopathy presentation in old age.

Mirhosseini SA, Mirhosseini SM, Bidaki R, Boshrabadi AP - J Res Med Sci (2013)

Bottom Line: She was referred to a neurosurgeon by a neurologist because of her progressive gait ataxia.Risk for brachial plexus injury because of compression or stretching by the clavicle accelerate with age.Therefore, the surgical approach of adults' patients with Sprengel's deformity can intend suitable surgical conclusions.

View Article: PubMed Central - PubMed

Affiliation: Department of Neurosurgery, Isfahan, Iran.

ABSTRACT
Klippel-Feil syndrome is a rare condition characterized by the congenital fusion of two of the seventh cervical vertebrae. A 50-year-old woman presented with a 2-year history of neck pain and ataxia for 1 year. She had not urinary incontinence. She was referred to a neurosurgeon by a neurologist because of her progressive gait ataxia. Risk for brachial plexus injury because of compression or stretching by the clavicle accelerate with age. Therefore, the surgical approach of adults' patients with Sprengel's deformity can intend suitable surgical conclusions.

No MeSH data available.


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(a) Computed tomography (b) oblique view CT postroanterior view
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Figure 2: (a) Computed tomography (b) oblique view CT postroanterior view

Mentions: Neurological examination showed intact cranial nerves and no motor deficit, but we found impairment in pain sensory and light touch in both legs that was prominent on the right side of the body, hyperreflexia in the left knee, ankle jerk, and mild gait ataxia based on tandem and blind walking. Blood tests and urinalysis were normal. Physical examination revealed a short neck, a low occipital hairline and diminished cervical range of motion. The patient also had an elevated left scapula and a bony prominence extending from the shoulder to the neck. The range of motion of the neck and left shoulder was restricted. Anteroposterior and lateral radiographs revealed fused vertebral body of C5-C6 without spina bifida [Figures 1, 2a and b].


Sprengel deformity and Klippel-Feil syndrome leading to cervical myelopathy presentation in old age.

Mirhosseini SA, Mirhosseini SM, Bidaki R, Boshrabadi AP - J Res Med Sci (2013)

(a) Computed tomography (b) oblique view CT postroanterior view
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC3818627&req=5

Figure 2: (a) Computed tomography (b) oblique view CT postroanterior view
Mentions: Neurological examination showed intact cranial nerves and no motor deficit, but we found impairment in pain sensory and light touch in both legs that was prominent on the right side of the body, hyperreflexia in the left knee, ankle jerk, and mild gait ataxia based on tandem and blind walking. Blood tests and urinalysis were normal. Physical examination revealed a short neck, a low occipital hairline and diminished cervical range of motion. The patient also had an elevated left scapula and a bony prominence extending from the shoulder to the neck. The range of motion of the neck and left shoulder was restricted. Anteroposterior and lateral radiographs revealed fused vertebral body of C5-C6 without spina bifida [Figures 1, 2a and b].

Bottom Line: She was referred to a neurosurgeon by a neurologist because of her progressive gait ataxia.Risk for brachial plexus injury because of compression or stretching by the clavicle accelerate with age.Therefore, the surgical approach of adults' patients with Sprengel's deformity can intend suitable surgical conclusions.

View Article: PubMed Central - PubMed

Affiliation: Department of Neurosurgery, Isfahan, Iran.

ABSTRACT
Klippel-Feil syndrome is a rare condition characterized by the congenital fusion of two of the seventh cervical vertebrae. A 50-year-old woman presented with a 2-year history of neck pain and ataxia for 1 year. She had not urinary incontinence. She was referred to a neurosurgeon by a neurologist because of her progressive gait ataxia. Risk for brachial plexus injury because of compression or stretching by the clavicle accelerate with age. Therefore, the surgical approach of adults' patients with Sprengel's deformity can intend suitable surgical conclusions.

No MeSH data available.


Related in: MedlinePlus