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Ankylosis of the hips and knees due to sickle cell disease.

Al Elayan SS, Al Hamdan A - F1000Res (2012)

Bottom Line: The patient's hemoglobin S decreased to levels below 30% by exchange transfusion.Bilateral total hip replacement, as well as unilateral total knee replacement, was carried out to improve his level of function.These complications were successfully managed and the patient was able to move and transfer using a wheel chair.

View Article: PubMed Central - PubMed

Affiliation: Department of Orthopedics, Prince Sultan Military Medical City, Riyadh, 11612, Saudi Arabia.

ABSTRACT
This is a case report of a 29-year-old Saudi male with sickle cell disease (SCD) with severe stiffness of his joints, mainly both knees and hips, secondary to complications of SCD. He was severely crippled: unable to sit, stand or walk, and was bedridden for 8 years when he was presented to us. Radiographs showed fusion of both knees and hips. There was no evidence of active osteomyelitis by Gallium scan. The patient's hemoglobin S decreased to levels below 30% by exchange transfusion. Bilateral total hip replacement, as well as unilateral total knee replacement, was carried out to improve his level of function. There is only one reported case of such severe and multiple joint complications in a single patient suffering from SCD. The increased life expectancy that medical advances have offered to the sickle-cell patients has led to the appearance of sickle-cell-related complications, which were previously only seen rarely. These complications were successfully managed and the patient was able to move and transfer using a wheel chair.

No MeSH data available.


Related in: MedlinePlus

AP pelvis x-ray post bilateral THR.
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f3: AP pelvis x-ray post bilateral THR.

Mentions: The patient was operated on with an aim to provide movement at the hips and knees and to recover his ability to sit, stand, transfer, balance and improves personal hygiene. Bilateral THR was done successfully (Figure 3). The procedures were performed utilizing the Harding lateral approach. Particular attention was paid to padding bony prominences and skin care in view of his poor skin condition. Intraoperatively, the bone was noted to be very fragile. The patient was kept in the intensive care unit for two days post operatively for observation and pain control. Post bilateral THR, the patient had marked improvement of hip flexion bilaterally permitting easy functional sitting. Post surgery physiotherapy resulted in great improvement in his general physical activity.


Ankylosis of the hips and knees due to sickle cell disease.

Al Elayan SS, Al Hamdan A - F1000Res (2012)

AP pelvis x-ray post bilateral THR.
© Copyright Policy - open-access
Related In: Results  -  Collection

License 1 - License 2
Show All Figures
getmorefigures.php?uid=PMC3814913&req=5

f3: AP pelvis x-ray post bilateral THR.
Mentions: The patient was operated on with an aim to provide movement at the hips and knees and to recover his ability to sit, stand, transfer, balance and improves personal hygiene. Bilateral THR was done successfully (Figure 3). The procedures were performed utilizing the Harding lateral approach. Particular attention was paid to padding bony prominences and skin care in view of his poor skin condition. Intraoperatively, the bone was noted to be very fragile. The patient was kept in the intensive care unit for two days post operatively for observation and pain control. Post bilateral THR, the patient had marked improvement of hip flexion bilaterally permitting easy functional sitting. Post surgery physiotherapy resulted in great improvement in his general physical activity.

Bottom Line: The patient's hemoglobin S decreased to levels below 30% by exchange transfusion.Bilateral total hip replacement, as well as unilateral total knee replacement, was carried out to improve his level of function.These complications were successfully managed and the patient was able to move and transfer using a wheel chair.

View Article: PubMed Central - PubMed

Affiliation: Department of Orthopedics, Prince Sultan Military Medical City, Riyadh, 11612, Saudi Arabia.

ABSTRACT
This is a case report of a 29-year-old Saudi male with sickle cell disease (SCD) with severe stiffness of his joints, mainly both knees and hips, secondary to complications of SCD. He was severely crippled: unable to sit, stand or walk, and was bedridden for 8 years when he was presented to us. Radiographs showed fusion of both knees and hips. There was no evidence of active osteomyelitis by Gallium scan. The patient's hemoglobin S decreased to levels below 30% by exchange transfusion. Bilateral total hip replacement, as well as unilateral total knee replacement, was carried out to improve his level of function. There is only one reported case of such severe and multiple joint complications in a single patient suffering from SCD. The increased life expectancy that medical advances have offered to the sickle-cell patients has led to the appearance of sickle-cell-related complications, which were previously only seen rarely. These complications were successfully managed and the patient was able to move and transfer using a wheel chair.

No MeSH data available.


Related in: MedlinePlus