Limits...
Combined cutaneous findings with segmental odontomaxillary dysplasia: Review of the literature and proposal of a new clinical classification.

Yassin OM, Rihani FB - Int Med Case Rep J (2008)

Bottom Line: He presented with left midfacial diffuse hyperkeratotic erythematous lesion, ipsilateral hypopigmentation of upper lip with indistinct vermilion border, left-sided facial swelling, unilateral maxillary enlargement and ipsilateral failure of eruption of permanent teeth.Radiographic imaging showed abnormal bony trabeculation, impacted and missing teeth.Clinicians should be aware of its presence when encountering patients presenting with a facial cutaneous lesion especially when it is associated with facial asymmetry and unresponsive to treatment.

View Article: PubMed Central - PubMed

Affiliation: Consultant in pediatric dentistry, Chairman of Pediatric Dentistry Specialty at King Hussien Medical Center, Royal Medical Services, Amman, Jordan.

ABSTRACT
Segmental odontomaxillary dysplasia is characterized by variability of its clinical and radiological features, and may mimic other fibro-osseous lesions. We describe the case of a segmental odontomaxillary dysplasia in a 12-year-old male comprising of dermal, gingival, bony, and dental abnormalities. He presented with left midfacial diffuse hyperkeratotic erythematous lesion, ipsilateral hypopigmentation of upper lip with indistinct vermilion border, left-sided facial swelling, unilateral maxillary enlargement and ipsilateral failure of eruption of permanent teeth. Radiographic imaging showed abnormal bony trabeculation, impacted and missing teeth. Histopathologic findings showed characteristic features of segmental odontomaxillary dysplasia. We herein report a case of this rare unusual anomaly, review the literature, and propose a new clinical classification based on the limited number of previously reported cases in an attempt to categorize the clinical variants of the condition which might be helpful when treatment options are to be considered. Clinicians should be aware of its presence when encountering patients presenting with a facial cutaneous lesion especially when it is associated with facial asymmetry and unresponsive to treatment.

No MeSH data available.


Related in: MedlinePlus

Orthopantomogram showing radiopacity with irregular bone trabecular pattern distal to maxillary left permanent canine. Note also reduction of size of ipsilateral maxillary sinus, absent left second premolar and abnormal root morphology of left deciduous and permanent molars.
© Copyright Policy
Related In: Results  -  Collection


getmorefigures.php?uid=PMC3643048&req=5

f3-imcrj-1-7: Orthopantomogram showing radiopacity with irregular bone trabecular pattern distal to maxillary left permanent canine. Note also reduction of size of ipsilateral maxillary sinus, absent left second premolar and abnormal root morphology of left deciduous and permanent molars.

Mentions: An orthopantomogram showed irregular bone trabecular pattern of the left maxilla from the maxillary left permanent lateral incisor region to the ipsilateral maxillary tuberosity. The floor of the left maxillary sinus was partially elevated when compared to the contralateral side. The maxillary left second premolar was missing and the maxillary left permanent canine was ectopically displaced. Other teeth within the lesion showed delayed or absent root development (Figure 3).


Combined cutaneous findings with segmental odontomaxillary dysplasia: Review of the literature and proposal of a new clinical classification.

Yassin OM, Rihani FB - Int Med Case Rep J (2008)

Orthopantomogram showing radiopacity with irregular bone trabecular pattern distal to maxillary left permanent canine. Note also reduction of size of ipsilateral maxillary sinus, absent left second premolar and abnormal root morphology of left deciduous and permanent molars.
© Copyright Policy
Related In: Results  -  Collection

Show All Figures
getmorefigures.php?uid=PMC3643048&req=5

f3-imcrj-1-7: Orthopantomogram showing radiopacity with irregular bone trabecular pattern distal to maxillary left permanent canine. Note also reduction of size of ipsilateral maxillary sinus, absent left second premolar and abnormal root morphology of left deciduous and permanent molars.
Mentions: An orthopantomogram showed irregular bone trabecular pattern of the left maxilla from the maxillary left permanent lateral incisor region to the ipsilateral maxillary tuberosity. The floor of the left maxillary sinus was partially elevated when compared to the contralateral side. The maxillary left second premolar was missing and the maxillary left permanent canine was ectopically displaced. Other teeth within the lesion showed delayed or absent root development (Figure 3).

Bottom Line: He presented with left midfacial diffuse hyperkeratotic erythematous lesion, ipsilateral hypopigmentation of upper lip with indistinct vermilion border, left-sided facial swelling, unilateral maxillary enlargement and ipsilateral failure of eruption of permanent teeth.Radiographic imaging showed abnormal bony trabeculation, impacted and missing teeth.Clinicians should be aware of its presence when encountering patients presenting with a facial cutaneous lesion especially when it is associated with facial asymmetry and unresponsive to treatment.

View Article: PubMed Central - PubMed

Affiliation: Consultant in pediatric dentistry, Chairman of Pediatric Dentistry Specialty at King Hussien Medical Center, Royal Medical Services, Amman, Jordan.

ABSTRACT
Segmental odontomaxillary dysplasia is characterized by variability of its clinical and radiological features, and may mimic other fibro-osseous lesions. We describe the case of a segmental odontomaxillary dysplasia in a 12-year-old male comprising of dermal, gingival, bony, and dental abnormalities. He presented with left midfacial diffuse hyperkeratotic erythematous lesion, ipsilateral hypopigmentation of upper lip with indistinct vermilion border, left-sided facial swelling, unilateral maxillary enlargement and ipsilateral failure of eruption of permanent teeth. Radiographic imaging showed abnormal bony trabeculation, impacted and missing teeth. Histopathologic findings showed characteristic features of segmental odontomaxillary dysplasia. We herein report a case of this rare unusual anomaly, review the literature, and propose a new clinical classification based on the limited number of previously reported cases in an attempt to categorize the clinical variants of the condition which might be helpful when treatment options are to be considered. Clinicians should be aware of its presence when encountering patients presenting with a facial cutaneous lesion especially when it is associated with facial asymmetry and unresponsive to treatment.

No MeSH data available.


Related in: MedlinePlus