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Congenital cystic adenomatoid malformation with bronchial atresia in elderly patients.

Kwak HJ, Moon JY, Kim SI, Kim TH, Sohn JW, Kim SH, Shin DH, Park SS, Chung WS, Yoon HJ - Tuberc Respir Dis (Seoul) (2012)

Bottom Line: CCAM type I is rarely found in association with bronchial atresia (BA) in adults; we present such a case.A 54-year-old female presented with chronic cough and blood-tinged sputum.Based on the radiologic findings, right middle lobectomy and a medial basal segmentectomy of the right lower lobe were performed via a thoracotomy.

View Article: PubMed Central - PubMed

Affiliation: Department of Internal Medicine, Hanyang University College of Medicine, Seoul, Korea.

ABSTRACT

Unlabelled: Congenital cystic adenomatoid malformation (CCAM) is an uncommon, nonhereditary anomaly caused by arrest of lung. Patients with CCAM may present with respiratory distress as newborns, or may remain asymptomatic until later in life. CCAM type I is rarely found in association with bronchial atresia (BA) in adults; we present such a case.

Case: A 54-year-old female presented with chronic cough and blood-tinged sputum. Physical examination and laboratory tests were unremarkable. Chest radiographs and a CT scan of the chest showed multiple large air-filled cysts consistent with a CCAM in the right lower lobe, and an oval-shaped opacity in the distal right middle lobal bronchus. Based on the radiologic findings, right middle lobectomy and a medial basal segmentectomy of the right lower lobe were performed via a thoracotomy. These lesions were consistent with Stocker's Type I CCAM and BA in the different lobes.

No MeSH data available.


Related in: MedlinePlus

Simple chest radiography on admission. A patch of opacity is seen in the right lower lung field (arrow).
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Figure 1: Simple chest radiography on admission. A patch of opacity is seen in the right lower lung field (arrow).

Mentions: Simple chest radiographs revealed a patchy opacity with multiple thin-walled cystic structures in the right lower lobe of the lung field (Figure 1). A computed tomography (CT) scan of the chest showed multiple large air-filled cystic lesions in the right lower lobe, which measured 12.0×11.0×5.5 cm3 in aggregate and were primarily located in the right lower lobe. At its perimeter were many small, fluid-filled spaces, the largest of which measured 1.5×1.0×1.0 cm3, and there was some calcification. These radiologic findings were consistent with type I CCAM (Figure 2A). Moreover, an oval-shaped opacity in the distal right middle lobe bronchus was surrounded by a low attenuation in the right middle lobe and there was no clear connection between the lesion and the tracheobronchial tree (Figure 2B); this was suggestive of BA. The other lung parenchyma was normal.


Congenital cystic adenomatoid malformation with bronchial atresia in elderly patients.

Kwak HJ, Moon JY, Kim SI, Kim TH, Sohn JW, Kim SH, Shin DH, Park SS, Chung WS, Yoon HJ - Tuberc Respir Dis (Seoul) (2012)

Simple chest radiography on admission. A patch of opacity is seen in the right lower lung field (arrow).
© Copyright Policy - open-access
Related In: Results  -  Collection

License 1 - License 2
Show All Figures
getmorefigures.php?uid=PMC3475458&req=5

Figure 1: Simple chest radiography on admission. A patch of opacity is seen in the right lower lung field (arrow).
Mentions: Simple chest radiographs revealed a patchy opacity with multiple thin-walled cystic structures in the right lower lobe of the lung field (Figure 1). A computed tomography (CT) scan of the chest showed multiple large air-filled cystic lesions in the right lower lobe, which measured 12.0×11.0×5.5 cm3 in aggregate and were primarily located in the right lower lobe. At its perimeter were many small, fluid-filled spaces, the largest of which measured 1.5×1.0×1.0 cm3, and there was some calcification. These radiologic findings were consistent with type I CCAM (Figure 2A). Moreover, an oval-shaped opacity in the distal right middle lobe bronchus was surrounded by a low attenuation in the right middle lobe and there was no clear connection between the lesion and the tracheobronchial tree (Figure 2B); this was suggestive of BA. The other lung parenchyma was normal.

Bottom Line: CCAM type I is rarely found in association with bronchial atresia (BA) in adults; we present such a case.A 54-year-old female presented with chronic cough and blood-tinged sputum.Based on the radiologic findings, right middle lobectomy and a medial basal segmentectomy of the right lower lobe were performed via a thoracotomy.

View Article: PubMed Central - PubMed

Affiliation: Department of Internal Medicine, Hanyang University College of Medicine, Seoul, Korea.

ABSTRACT

Unlabelled: Congenital cystic adenomatoid malformation (CCAM) is an uncommon, nonhereditary anomaly caused by arrest of lung. Patients with CCAM may present with respiratory distress as newborns, or may remain asymptomatic until later in life. CCAM type I is rarely found in association with bronchial atresia (BA) in adults; we present such a case.

Case: A 54-year-old female presented with chronic cough and blood-tinged sputum. Physical examination and laboratory tests were unremarkable. Chest radiographs and a CT scan of the chest showed multiple large air-filled cysts consistent with a CCAM in the right lower lobe, and an oval-shaped opacity in the distal right middle lobal bronchus. Based on the radiologic findings, right middle lobectomy and a medial basal segmentectomy of the right lower lobe were performed via a thoracotomy. These lesions were consistent with Stocker's Type I CCAM and BA in the different lobes.

No MeSH data available.


Related in: MedlinePlus