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Bilateral congenital choanal atresia and osteoma of ethmoid sinus with supernumerary nostril: a case report and review of the literature.

Li XZ, Cai XL, Zhang L, Han XF, Wei X - J Med Case Rep (2011)

Bottom Line: A 22-year-old Chinese man presented with mouth breathing, sleep snoring and difficult feeding after birth, with no olfactory sensation.Three-dimensional computed tomography revealed bilateral choanal atresia and a high density bony shadow in his left ethmoid sinus that extended to his left frontal sinus.To the best of our knowledge, this is the first report of choanal atresia accompanied by congenital accessory nasal deformity and congenital keratoleukoma.

View Article: PubMed Central - HTML - PubMed

Affiliation: Department of Otolaryngology, Qilu Hospital, Shandong University, Ji'nan 250012, China. zhangleicome@126.com.

ABSTRACT

Introduction: Congenital choanal atresia is a relatively rare deformity, especially bilateral congenital choanal atresia. We report a case of bilateral congenital choanal atresia in a 22-year-old Chinese man, who was also diagnosed with congenital right accessory nasal deformity, osteoma of his left ethmoid sinus and congenital keratoleukoma of his right eye.

Case presentation: A 22-year-old Chinese man presented with mouth breathing, sleep snoring and difficult feeding after birth, with no olfactory sensation. Three-dimensional computed tomography revealed bilateral choanal atresia and a high density bony shadow in his left ethmoid sinus that extended to his left frontal sinus.

Conclusions: Choanal atresia is often accompanied by other congenital abnormalities. To the best of our knowledge, this is the first report of choanal atresia accompanied by congenital accessory nasal deformity and congenital keratoleukoma.

No MeSH data available.


Related in: MedlinePlus

Microphotograph of the tumor. Hematoxylin and eosin stain (original magnification ×20).
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Figure 8: Microphotograph of the tumor. Hematoxylin and eosin stain (original magnification ×20).

Mentions: Under nasal endoscopy, the uncinate process, ethmoid bulla and air cells were removed. The maxillary sinus ostium was opened to locate the plane of the lamina papyracea. Then, inside the ethmoid sinus, a white bony mass was identified clearly (Figure 7) and resected completely. The bony mass was irregular in shape, pale in color, and difficult to remove from the middle meatus. Its size was about 2.2 cm × 1.8 cm × 2.0 cm. The roof of the ethmoid and cribriform plate was examined carefully and found to be intact. Neither leakage of cerebrospinal fluid nor active bleeding occurred. Dense osteocarcinoma was diagnosed by postoperative pathology (Figure 8).


Bilateral congenital choanal atresia and osteoma of ethmoid sinus with supernumerary nostril: a case report and review of the literature.

Li XZ, Cai XL, Zhang L, Han XF, Wei X - J Med Case Rep (2011)

Microphotograph of the tumor. Hematoxylin and eosin stain (original magnification ×20).
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC3285051&req=5

Figure 8: Microphotograph of the tumor. Hematoxylin and eosin stain (original magnification ×20).
Mentions: Under nasal endoscopy, the uncinate process, ethmoid bulla and air cells were removed. The maxillary sinus ostium was opened to locate the plane of the lamina papyracea. Then, inside the ethmoid sinus, a white bony mass was identified clearly (Figure 7) and resected completely. The bony mass was irregular in shape, pale in color, and difficult to remove from the middle meatus. Its size was about 2.2 cm × 1.8 cm × 2.0 cm. The roof of the ethmoid and cribriform plate was examined carefully and found to be intact. Neither leakage of cerebrospinal fluid nor active bleeding occurred. Dense osteocarcinoma was diagnosed by postoperative pathology (Figure 8).

Bottom Line: A 22-year-old Chinese man presented with mouth breathing, sleep snoring and difficult feeding after birth, with no olfactory sensation.Three-dimensional computed tomography revealed bilateral choanal atresia and a high density bony shadow in his left ethmoid sinus that extended to his left frontal sinus.To the best of our knowledge, this is the first report of choanal atresia accompanied by congenital accessory nasal deformity and congenital keratoleukoma.

View Article: PubMed Central - HTML - PubMed

Affiliation: Department of Otolaryngology, Qilu Hospital, Shandong University, Ji'nan 250012, China. zhangleicome@126.com.

ABSTRACT

Introduction: Congenital choanal atresia is a relatively rare deformity, especially bilateral congenital choanal atresia. We report a case of bilateral congenital choanal atresia in a 22-year-old Chinese man, who was also diagnosed with congenital right accessory nasal deformity, osteoma of his left ethmoid sinus and congenital keratoleukoma of his right eye.

Case presentation: A 22-year-old Chinese man presented with mouth breathing, sleep snoring and difficult feeding after birth, with no olfactory sensation. Three-dimensional computed tomography revealed bilateral choanal atresia and a high density bony shadow in his left ethmoid sinus that extended to his left frontal sinus.

Conclusions: Choanal atresia is often accompanied by other congenital abnormalities. To the best of our knowledge, this is the first report of choanal atresia accompanied by congenital accessory nasal deformity and congenital keratoleukoma.

No MeSH data available.


Related in: MedlinePlus