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Rubinstein-Taybi syndrome with scoliosis.

Tatara Y, Kawakami N, Tsuji T, Miyasaka K, Ohara T, Nohara A - Scoliosis (2011)

Bottom Line: To avoid respiratory complications, the patient was put on a respirator in the ICU for several days after both surgeries.No postoperative complications occurred after both surgeries.We succeeded in treating the patient without complications.

View Article: PubMed Central - HTML - PubMed

Affiliation: Meijo Hospital, Spine Center, Nagoya, Aichi, Japan. nupriver@gmail.com.

ABSTRACT

Study design: Case report.

Objective: The authors present the case of a 14-year-old boy with Rubinstein-Taybi syndrome (RSTS) presenting scoliosis.

Summary of background data: There have been no reports on surgery for RSTS presenting scoliosis.

Methods: The patient was referred to our hospital for evaluation of a progressive spinal curvature. A standing anteroposterior spine radiograph at presentation to our hospital revealed an 84-degree right thoracic curve from T6 to T12, along with a 63-degree left lumbar compensatory curve from T12 to L4. We planned a two-staged surgery and decided to fuse from T4 to L4. The first operation was front-back surgery because of the rigidity of the right thoracic curve. The second operation of lumbar anterior discectomy and fusion was arranged 9 months after the first surgery to prevent the crankshaft phenomenon due to his natural course of adolescent growth. To avoid respiratory complications, the patient was put on a respirator in the ICU for several days after both surgeries.

Results: Full-length spine radiographs after the first surgery revealed no instrumentation failure and showed that the right thoracic curve was corrected to 31 degrees and the left lumbar curve was corrected to 34 degrees. No postoperative complications occurred after both surgeries.

Conclusions: We succeeded in treating the patient without complications. Full-length spine standing radiographs at one year after the second operation demonstrated a stable bony arthrodesis with no loss of initial correction.

No MeSH data available.


Related in: MedlinePlus

Full-length spine standing radiographs at one year after the second operation. The initial correction is maintained. The Cobb angle from T6 to T12 is 31 degrees and the angle from T12 to L4 is 34 degrees. Left: coronal, Right: sagittal.
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Figure 3: Full-length spine standing radiographs at one year after the second operation. The initial correction is maintained. The Cobb angle from T6 to T12 is 31 degrees and the angle from T12 to L4 is 34 degrees. Left: coronal, Right: sagittal.

Mentions: He entered the ICU immediately after both the first and second surgeries and was maintained on a respirator for several days in order to prevent respiratory complications. The patient wore a thoracolumbar spinal orthosis for 6 months after the first surgery. Full-length spine standing radiographs at one year after the second operation demonstrated a stable bony arthrodesis with no loss of initial correction (Figure 3 L and R). His parents consented to submitting data from the case for publication.


Rubinstein-Taybi syndrome with scoliosis.

Tatara Y, Kawakami N, Tsuji T, Miyasaka K, Ohara T, Nohara A - Scoliosis (2011)

Full-length spine standing radiographs at one year after the second operation. The initial correction is maintained. The Cobb angle from T6 to T12 is 31 degrees and the angle from T12 to L4 is 34 degrees. Left: coronal, Right: sagittal.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC3198739&req=5

Figure 3: Full-length spine standing radiographs at one year after the second operation. The initial correction is maintained. The Cobb angle from T6 to T12 is 31 degrees and the angle from T12 to L4 is 34 degrees. Left: coronal, Right: sagittal.
Mentions: He entered the ICU immediately after both the first and second surgeries and was maintained on a respirator for several days in order to prevent respiratory complications. The patient wore a thoracolumbar spinal orthosis for 6 months after the first surgery. Full-length spine standing radiographs at one year after the second operation demonstrated a stable bony arthrodesis with no loss of initial correction (Figure 3 L and R). His parents consented to submitting data from the case for publication.

Bottom Line: To avoid respiratory complications, the patient was put on a respirator in the ICU for several days after both surgeries.No postoperative complications occurred after both surgeries.We succeeded in treating the patient without complications.

View Article: PubMed Central - HTML - PubMed

Affiliation: Meijo Hospital, Spine Center, Nagoya, Aichi, Japan. nupriver@gmail.com.

ABSTRACT

Study design: Case report.

Objective: The authors present the case of a 14-year-old boy with Rubinstein-Taybi syndrome (RSTS) presenting scoliosis.

Summary of background data: There have been no reports on surgery for RSTS presenting scoliosis.

Methods: The patient was referred to our hospital for evaluation of a progressive spinal curvature. A standing anteroposterior spine radiograph at presentation to our hospital revealed an 84-degree right thoracic curve from T6 to T12, along with a 63-degree left lumbar compensatory curve from T12 to L4. We planned a two-staged surgery and decided to fuse from T4 to L4. The first operation was front-back surgery because of the rigidity of the right thoracic curve. The second operation of lumbar anterior discectomy and fusion was arranged 9 months after the first surgery to prevent the crankshaft phenomenon due to his natural course of adolescent growth. To avoid respiratory complications, the patient was put on a respirator in the ICU for several days after both surgeries.

Results: Full-length spine radiographs after the first surgery revealed no instrumentation failure and showed that the right thoracic curve was corrected to 31 degrees and the left lumbar curve was corrected to 34 degrees. No postoperative complications occurred after both surgeries.

Conclusions: We succeeded in treating the patient without complications. Full-length spine standing radiographs at one year after the second operation demonstrated a stable bony arthrodesis with no loss of initial correction.

No MeSH data available.


Related in: MedlinePlus