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Successful management of aggressive fibromatosis of the neck using wide surgical excision: a case report.

Sobani ZA, Junaid M, Khan MJ - J Med Case Rep (2011)

Bottom Line: Aggressive fibromatosis is a benign tumor, thought to arise from deep musculoaponeurotic structures, rarely found in the head or neck.However, when it does occur in the head and neck region, it tends to be more aggressive and associated with significant morbidity, which may be attributed to the vital vascular, neurological or anatomical structures in close proximity.We report the case of a 39-year-old Pakistani man who presented with a two-month history of a lump on the right side of his neck.

View Article: PubMed Central - HTML - PubMed

Affiliation: Medical College, Aga Khan University, Stadium Road, Karachi, Pakistan. zsobani@gmail.com.

ABSTRACT

Introduction: Aggressive fibromatosis is a benign tumor, thought to arise from deep musculoaponeurotic structures, rarely found in the head or neck. However, when it does occur in the head and neck region, it tends to be more aggressive and associated with significant morbidity, which may be attributed to the vital vascular, neurological or anatomical structures in close proximity.

Case presentation: We report the case of a 39-year-old Pakistani man who presented with a two-month history of a lump on the right side of his neck. The mass was excised and histopathological analysis revealed a case of aggressive fibromatosis.

Conclusion: Due to the rarity of the condition no guidelines are available on the indications and extent of each modality. Due to its aggressive behavior and tendency to invade local structures and recur, a multi-modality management strategy is usually employed. On the basis of this case, we suggest that aggressive surgery is a viable management option and may be successfully used as a single modality treatment.

No MeSH data available.


Related in: MedlinePlus

Coronal (A), axial (B) and sagittal (C) CT scans with contrast showing the mass measuring about 9.3 × 5.9 × 12 cm with areas of central necrosis. The carotid sheath is displaced anteriorly.
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Figure 3: Coronal (A), axial (B) and sagittal (C) CT scans with contrast showing the mass measuring about 9.3 × 5.9 × 12 cm with areas of central necrosis. The carotid sheath is displaced anteriorly.

Mentions: Magnetic resonance imaging (MRI) showed a large contrast-enhancing mass, hypointense on T1 and hyperintense on T2, lying in the lower part of his neck to the right of the midline. It was deep to the SCM on the anterior side, abutting the larynx medially and the paravertebral muscles and space on the posterior side [Figure 2]. A CT scan showed a large soft tissue density mass measuring about 9.3 × 5.9 × 12 cm, with central necrosis consistent with recurrent fibromatosis in the posterior triangle [Figure 3].


Successful management of aggressive fibromatosis of the neck using wide surgical excision: a case report.

Sobani ZA, Junaid M, Khan MJ - J Med Case Rep (2011)

Coronal (A), axial (B) and sagittal (C) CT scans with contrast showing the mass measuring about 9.3 × 5.9 × 12 cm with areas of central necrosis. The carotid sheath is displaced anteriorly.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC3141701&req=5

Figure 3: Coronal (A), axial (B) and sagittal (C) CT scans with contrast showing the mass measuring about 9.3 × 5.9 × 12 cm with areas of central necrosis. The carotid sheath is displaced anteriorly.
Mentions: Magnetic resonance imaging (MRI) showed a large contrast-enhancing mass, hypointense on T1 and hyperintense on T2, lying in the lower part of his neck to the right of the midline. It was deep to the SCM on the anterior side, abutting the larynx medially and the paravertebral muscles and space on the posterior side [Figure 2]. A CT scan showed a large soft tissue density mass measuring about 9.3 × 5.9 × 12 cm, with central necrosis consistent with recurrent fibromatosis in the posterior triangle [Figure 3].

Bottom Line: Aggressive fibromatosis is a benign tumor, thought to arise from deep musculoaponeurotic structures, rarely found in the head or neck.However, when it does occur in the head and neck region, it tends to be more aggressive and associated with significant morbidity, which may be attributed to the vital vascular, neurological or anatomical structures in close proximity.We report the case of a 39-year-old Pakistani man who presented with a two-month history of a lump on the right side of his neck.

View Article: PubMed Central - HTML - PubMed

Affiliation: Medical College, Aga Khan University, Stadium Road, Karachi, Pakistan. zsobani@gmail.com.

ABSTRACT

Introduction: Aggressive fibromatosis is a benign tumor, thought to arise from deep musculoaponeurotic structures, rarely found in the head or neck. However, when it does occur in the head and neck region, it tends to be more aggressive and associated with significant morbidity, which may be attributed to the vital vascular, neurological or anatomical structures in close proximity.

Case presentation: We report the case of a 39-year-old Pakistani man who presented with a two-month history of a lump on the right side of his neck. The mass was excised and histopathological analysis revealed a case of aggressive fibromatosis.

Conclusion: Due to the rarity of the condition no guidelines are available on the indications and extent of each modality. Due to its aggressive behavior and tendency to invade local structures and recur, a multi-modality management strategy is usually employed. On the basis of this case, we suggest that aggressive surgery is a viable management option and may be successfully used as a single modality treatment.

No MeSH data available.


Related in: MedlinePlus