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Hemangioma related to Maffucci syndrome in a man: a case report.

Kondo T - J Med Case Rep (2011)

Bottom Line: One of the hemangiomas was removed and examined pathologically.The morphological picture was an admixture of cavernous hemangioma and spindle cell hemangioma without cytological atypia or mitosis.Sheets of vacuolated endothelial cells were also observed.

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Affiliation: Division of Legal Medicine, Department of Community Medicine and Social Healthcare Science, Kobe University Graduate School of Medicine, 7-5-1 Kusunoki-cho, Chuo-ku, Kobe 650-0017, Japan. kondo@med.kobe-u.ac.jp.

ABSTRACT

Introduction: Maffucci syndrome is a rare clinical entity (approximately 200 cases have been reported in the medical literature) with a combined occurrence of multiple enchondromas and vascular tumors.

Case presentation: The case of a 43-year-old Japanese man with multiple chondromas and hemangiomas (Maffucci syndrome) is reported. One of the hemangiomas was removed and examined pathologically. The morphological picture was an admixture of cavernous hemangioma and spindle cell hemangioma without cytological atypia or mitosis. Sheets of vacuolated endothelial cells were also observed.

Conclusion: A rare case of hemangioma associated with Maffucci syndrome, focusing on the pathologic nature of the submitted tissue, is reported.

No MeSH data available.


Related in: MedlinePlus

Macroscopic findings of the lesion. (A) The lesion had a serpentine appearance. (B) The cut surface of the lesion. It had a blackish area filled with blood and a whitish area.
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Figure 1: Macroscopic findings of the lesion. (A) The lesion had a serpentine appearance. (B) The cut surface of the lesion. It had a blackish area filled with blood and a whitish area.

Mentions: A 43-year-old Japanese man presented with multiple chondromas and hemangiomas. His disease had been diagnosed as Maffucci syndrome. His available clinical information, however, was limited. One of the hemangiomas was removed and examined pathologically. Macroscopically, the lesion showed a serpentine appearance (Figure 1A). The cut surface of the lesion showed a blackish area filled with blood and a whitish area (Figure 1B).


Hemangioma related to Maffucci syndrome in a man: a case report.

Kondo T - J Med Case Rep (2011)

Macroscopic findings of the lesion. (A) The lesion had a serpentine appearance. (B) The cut surface of the lesion. It had a blackish area filled with blood and a whitish area.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC3141690&req=5

Figure 1: Macroscopic findings of the lesion. (A) The lesion had a serpentine appearance. (B) The cut surface of the lesion. It had a blackish area filled with blood and a whitish area.
Mentions: A 43-year-old Japanese man presented with multiple chondromas and hemangiomas. His disease had been diagnosed as Maffucci syndrome. His available clinical information, however, was limited. One of the hemangiomas was removed and examined pathologically. Macroscopically, the lesion showed a serpentine appearance (Figure 1A). The cut surface of the lesion showed a blackish area filled with blood and a whitish area (Figure 1B).

Bottom Line: One of the hemangiomas was removed and examined pathologically.The morphological picture was an admixture of cavernous hemangioma and spindle cell hemangioma without cytological atypia or mitosis.Sheets of vacuolated endothelial cells were also observed.

View Article: PubMed Central - HTML - PubMed

Affiliation: Division of Legal Medicine, Department of Community Medicine and Social Healthcare Science, Kobe University Graduate School of Medicine, 7-5-1 Kusunoki-cho, Chuo-ku, Kobe 650-0017, Japan. kondo@med.kobe-u.ac.jp.

ABSTRACT

Introduction: Maffucci syndrome is a rare clinical entity (approximately 200 cases have been reported in the medical literature) with a combined occurrence of multiple enchondromas and vascular tumors.

Case presentation: The case of a 43-year-old Japanese man with multiple chondromas and hemangiomas (Maffucci syndrome) is reported. One of the hemangiomas was removed and examined pathologically. The morphological picture was an admixture of cavernous hemangioma and spindle cell hemangioma without cytological atypia or mitosis. Sheets of vacuolated endothelial cells were also observed.

Conclusion: A rare case of hemangioma associated with Maffucci syndrome, focusing on the pathologic nature of the submitted tissue, is reported.

No MeSH data available.


Related in: MedlinePlus