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Congenital hepatic fibrosis leading to cirrhosis and hepatocellular carcinoma: a case report.

Ghadir MR, Bagheri M, Ghanooni AH - J Med Case Rep (2011)

Bottom Line: Advanced cirrhosis was diagnosed and our patient was scheduled for liver transplantation.During preparation for transplant, a hepatic mass was discovered which was found to be hepatocellular carcinoma.Radiofrequency ablation was performed and our patient was referred for transplantation.

View Article: PubMed Central - HTML - PubMed

Affiliation: Qom University of Medical Sciences, Qom, Iran. ghadir@ddrc.ac.ir.

ABSTRACT

Introduction: Congenital hepatic fibrosis is an uncommon cause of portal hypertension. Despite the presence of portal hypertension, hepatocellular and renal function are usually well preserved. Congenital hepatic fibrosis is included in the group of congenital diseases of fibropolycystic disorders. These include a broad spectrum of clinical diseases which are usually accompanied by hepatic involvement.

Case presentation: We report the case of a 27-year-old Iranian woman with congenital hepatic fibrosis leading to cirrhosis and subsequently hepatocellular carcinoma.

Conclusion: Advanced cirrhosis was diagnosed and our patient was scheduled for liver transplantation. During preparation for transplant, a hepatic mass was discovered which was found to be hepatocellular carcinoma. Radiofrequency ablation was performed and our patient was referred for transplantation.

No MeSH data available.


Related in: MedlinePlus

Following radiofrequency ablation, tumor size declined.
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Figure 4: Following radiofrequency ablation, tumor size declined.

Mentions: Following radiofrequency ablation, the tumor size declined to about 25 mm with central necrosis (Figure 4) and our patient was enrolled on to the liver transplantation waiting list again.


Congenital hepatic fibrosis leading to cirrhosis and hepatocellular carcinoma: a case report.

Ghadir MR, Bagheri M, Ghanooni AH - J Med Case Rep (2011)

Following radiofrequency ablation, tumor size declined.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC3105948&req=5

Figure 4: Following radiofrequency ablation, tumor size declined.
Mentions: Following radiofrequency ablation, the tumor size declined to about 25 mm with central necrosis (Figure 4) and our patient was enrolled on to the liver transplantation waiting list again.

Bottom Line: Advanced cirrhosis was diagnosed and our patient was scheduled for liver transplantation.During preparation for transplant, a hepatic mass was discovered which was found to be hepatocellular carcinoma.Radiofrequency ablation was performed and our patient was referred for transplantation.

View Article: PubMed Central - HTML - PubMed

Affiliation: Qom University of Medical Sciences, Qom, Iran. ghadir@ddrc.ac.ir.

ABSTRACT

Introduction: Congenital hepatic fibrosis is an uncommon cause of portal hypertension. Despite the presence of portal hypertension, hepatocellular and renal function are usually well preserved. Congenital hepatic fibrosis is included in the group of congenital diseases of fibropolycystic disorders. These include a broad spectrum of clinical diseases which are usually accompanied by hepatic involvement.

Case presentation: We report the case of a 27-year-old Iranian woman with congenital hepatic fibrosis leading to cirrhosis and subsequently hepatocellular carcinoma.

Conclusion: Advanced cirrhosis was diagnosed and our patient was scheduled for liver transplantation. During preparation for transplant, a hepatic mass was discovered which was found to be hepatocellular carcinoma. Radiofrequency ablation was performed and our patient was referred for transplantation.

No MeSH data available.


Related in: MedlinePlus