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Frosted branch angiitis diagnosed as neuro-behçet: a diagnostic and etiologic dilemma.

Portero A, Herreras JM - Case Rep Ophthalmol (2011)

Bottom Line: Description, diagnosis, angiogram imaging and follow-up of a 28-year-old female with FBA. 'Frosted branch angiitis' is a clinical term applied to three conditions: infiltration of vessels by malignant cells, and sheathing of vessels either secondary to an active disorder or subsequently to a previous inflammatory disease.Our patient's history of two optic neuropathies and the lack of demyelinating signs in neuroimaging made us consider FBA in the context of neuro-Behçet.Recognition of the category of FBA from the clinical signs is essential to establish the correct diagnosis and prescribe the appropriate treatment.

View Article: PubMed Central - PubMed

Affiliation: Ophthalmology Department, University Hospital of Valladolid and IOBA, Valladolid, Spain.

ABSTRACT

Purpose: To report a case of frosted branch angiitis (FBA) secondary to neuro-Behçet.

Methods: Description, diagnosis, angiogram imaging and follow-up of a 28-year-old female with FBA.

Results: 'Frosted branch angiitis' is a clinical term applied to three conditions: infiltration of vessels by malignant cells, and sheathing of vessels either secondary to an active disorder or subsequently to a previous inflammatory disease. Our patient's history of two optic neuropathies and the lack of demyelinating signs in neuroimaging made us consider FBA in the context of neuro-Behçet.

Conclusion: Recognition of the category of FBA from the clinical signs is essential to establish the correct diagnosis and prescribe the appropriate treatment.

No MeSH data available.


Related in: MedlinePlus

Fundus and OCT images 4 months after the disorder started. In the upper figures, the retinographies show a mottling pattern at the foveal retinal pigment epithelium level resembling a macular hole which was ruled out with the OCT (both lower figures).
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Figure 2: Fundus and OCT images 4 months after the disorder started. In the upper figures, the retinographies show a mottling pattern at the foveal retinal pigment epithelium level resembling a macular hole which was ruled out with the OCT (both lower figures).

Mentions: The patient was kept on that regimen until 3 weeks later when steroids were tapered slowly during 3 months. Four months after her problems started, the patient presented a significant VA improvement (OD 20/20 and OS 20/20) and no intraocular inflammation. Ocular fundus imaging disclosed some hard exudates where macular stars were and mottling of the retinal pigment epithelium at the fovea level. FA only showed an ischemic zone in the temporal retina which produced a peripheral scotoma in the visual fields performed (fig. 2).


Frosted branch angiitis diagnosed as neuro-behçet: a diagnostic and etiologic dilemma.

Portero A, Herreras JM - Case Rep Ophthalmol (2011)

Fundus and OCT images 4 months after the disorder started. In the upper figures, the retinographies show a mottling pattern at the foveal retinal pigment epithelium level resembling a macular hole which was ruled out with the OCT (both lower figures).
© Copyright Policy - open-access
Related In: Results  -  Collection

License 1 - License 2
Show All Figures
getmorefigures.php?uid=PMC3104864&req=5

Figure 2: Fundus and OCT images 4 months after the disorder started. In the upper figures, the retinographies show a mottling pattern at the foveal retinal pigment epithelium level resembling a macular hole which was ruled out with the OCT (both lower figures).
Mentions: The patient was kept on that regimen until 3 weeks later when steroids were tapered slowly during 3 months. Four months after her problems started, the patient presented a significant VA improvement (OD 20/20 and OS 20/20) and no intraocular inflammation. Ocular fundus imaging disclosed some hard exudates where macular stars were and mottling of the retinal pigment epithelium at the fovea level. FA only showed an ischemic zone in the temporal retina which produced a peripheral scotoma in the visual fields performed (fig. 2).

Bottom Line: Description, diagnosis, angiogram imaging and follow-up of a 28-year-old female with FBA. 'Frosted branch angiitis' is a clinical term applied to three conditions: infiltration of vessels by malignant cells, and sheathing of vessels either secondary to an active disorder or subsequently to a previous inflammatory disease.Our patient's history of two optic neuropathies and the lack of demyelinating signs in neuroimaging made us consider FBA in the context of neuro-Behçet.Recognition of the category of FBA from the clinical signs is essential to establish the correct diagnosis and prescribe the appropriate treatment.

View Article: PubMed Central - PubMed

Affiliation: Ophthalmology Department, University Hospital of Valladolid and IOBA, Valladolid, Spain.

ABSTRACT

Purpose: To report a case of frosted branch angiitis (FBA) secondary to neuro-Behçet.

Methods: Description, diagnosis, angiogram imaging and follow-up of a 28-year-old female with FBA.

Results: 'Frosted branch angiitis' is a clinical term applied to three conditions: infiltration of vessels by malignant cells, and sheathing of vessels either secondary to an active disorder or subsequently to a previous inflammatory disease. Our patient's history of two optic neuropathies and the lack of demyelinating signs in neuroimaging made us consider FBA in the context of neuro-Behçet.

Conclusion: Recognition of the category of FBA from the clinical signs is essential to establish the correct diagnosis and prescribe the appropriate treatment.

No MeSH data available.


Related in: MedlinePlus