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Congenital isolated right radial club hand.

Salati SA, Rabah SM - Libyan J Med (2010)

Bottom Line: Congenital radial club hand (RCH) is an uncommon congenital anomaly characterized by various degrees of deficiency along the preaxial or radial side of the extremity.We present one such case of Type 4 congenital isolated RCH who presented to a tertiary care center in the Middle East.

View Article: PubMed Central - PubMed

Affiliation: Department of Plastic & Reconstructive Surgery, King Fahad Medical City, Riyadh, Saudi Arabia.

ABSTRACT
Congenital radial club hand (RCH) is an uncommon congenital anomaly characterized by various degrees of deficiency along the preaxial or radial side of the extremity. We present one such case of Type 4 congenital isolated RCH who presented to a tertiary care center in the Middle East.

No MeSH data available.


Related in: MedlinePlus

Right congenital radial club hand.
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Figure 0001: Right congenital radial club hand.

Mentions: A four-month-old male child was referred for evaluation of right upper limb deformity. He was born at term by normal delivery following an uneventful pregnancy and there was no significant past medical or surgical history. He was the first child of non-consanguineous parents and there was no family history of congenital anomalies. Physical examination of the baby revealed deformity of right forearm which appeared shorter than contra lateral side with radial deviation at the wrist (Fig. 1). All the fingers of the affected hand including the thumb were however normal. Physical examination by our team and by the pediatricians revealed no other abnormalities. Hemoglobin, total and differential leucocytes count, platelet count, and renal function tests were all within normal limits in more than one occasion. Radiographs of both upper limbs revealed complete aplasia of radius and shortening of the ulna on the right side (Fig. 2). Skeletal survey, ultrasonogram of abdomen, and cardiac echocardiogram ruled out any other associated congenital anomalies. The diagnosis of isolated right congenital radial club hand (RCH) Type IV was made and the parents were counseled. The management of the child was started in collaboration with physiotherapists and the family were taught some simple and easily reproducible exercises to passively stretch the radial structures. Custom-made splints were also fabricated by the orthotics division for nocturnal application to the affected limb with the aim of stretching the radial wrist structures. In future, when the level of deformity is deemed optimal for operative intervention (expected by age of one year), operative centralization of the wrist on ulna will be undertaken.


Congenital isolated right radial club hand.

Salati SA, Rabah SM - Libyan J Med (2010)

Right congenital radial club hand.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC3066786&req=5

Figure 0001: Right congenital radial club hand.
Mentions: A four-month-old male child was referred for evaluation of right upper limb deformity. He was born at term by normal delivery following an uneventful pregnancy and there was no significant past medical or surgical history. He was the first child of non-consanguineous parents and there was no family history of congenital anomalies. Physical examination of the baby revealed deformity of right forearm which appeared shorter than contra lateral side with radial deviation at the wrist (Fig. 1). All the fingers of the affected hand including the thumb were however normal. Physical examination by our team and by the pediatricians revealed no other abnormalities. Hemoglobin, total and differential leucocytes count, platelet count, and renal function tests were all within normal limits in more than one occasion. Radiographs of both upper limbs revealed complete aplasia of radius and shortening of the ulna on the right side (Fig. 2). Skeletal survey, ultrasonogram of abdomen, and cardiac echocardiogram ruled out any other associated congenital anomalies. The diagnosis of isolated right congenital radial club hand (RCH) Type IV was made and the parents were counseled. The management of the child was started in collaboration with physiotherapists and the family were taught some simple and easily reproducible exercises to passively stretch the radial structures. Custom-made splints were also fabricated by the orthotics division for nocturnal application to the affected limb with the aim of stretching the radial wrist structures. In future, when the level of deformity is deemed optimal for operative intervention (expected by age of one year), operative centralization of the wrist on ulna will be undertaken.

Bottom Line: Congenital radial club hand (RCH) is an uncommon congenital anomaly characterized by various degrees of deficiency along the preaxial or radial side of the extremity.We present one such case of Type 4 congenital isolated RCH who presented to a tertiary care center in the Middle East.

View Article: PubMed Central - PubMed

Affiliation: Department of Plastic & Reconstructive Surgery, King Fahad Medical City, Riyadh, Saudi Arabia.

ABSTRACT
Congenital radial club hand (RCH) is an uncommon congenital anomaly characterized by various degrees of deficiency along the preaxial or radial side of the extremity. We present one such case of Type 4 congenital isolated RCH who presented to a tertiary care center in the Middle East.

No MeSH data available.


Related in: MedlinePlus