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Congenital orbital lymphangioma in a 20-years old girl a case report and review of literature.

Mishra A, Abuhajar R, Alsawidi K, Alaoud M, Ehtuish E - Libyan J Med (2009)

Bottom Line: We report a case of a 20-year-old girl who presented to the out-patients' department with congenital, progressive unilateral proptosis and reduced vision.Diagnosis of orbital lymphangioma was made on imaging.This case is reported because of its extreme rarity and unusual presentation.

View Article: PubMed Central - PubMed

Affiliation: Department of Radiology, National Organ Transplant Centre, Central Hospital, Tripoli, Libya.

ABSTRACT
We report a case of a 20-year-old girl who presented to the out-patients' department with congenital, progressive unilateral proptosis and reduced vision. Ultrasound, computed tomography (CT) scan and magnetic resonance imaging (MRI) were performed. Diagnosis of orbital lymphangioma was made on imaging. Authors highlight the crucial role of imaging in diagnosis and to plan therapeutic approach. This case is reported because of its extreme rarity and unusual presentation.

No MeSH data available.


Related in: MedlinePlus

Coronal post-contrast CT scan thin section shows the retrobulbar non-enhancing lesions with preseptal extension.
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Figure 0003: Coronal post-contrast CT scan thin section shows the retrobulbar non-enhancing lesions with preseptal extension.

Mentions: A 20-year-old girl presented to the out-patients’ department with unilateral proptosis since birth. This was progressive in nature. There was also an ipsilateral facial deformity with fullness in the supraorbital space (Figure 1). There was no association with pain. There was no history of sudden increase of proptosis. In addition, there was a reduced vision 6/36 in the affected eye. The cornea was clear and so was the lens. Choroidal folds were seen on fundus examination with normal disc and macula. There was no history of redness of the eye. No watery discharge was seen. Ultrasound examination showed multiple cystic intraconal spaces (Figure 2) with very low but turbulent flow. CT scan showed multiple hypodense nonenhancing intraconal lobulated lesions extending into the preseptal space (Figure 3). MRI showed an unencapsulated homogenous lobulated intraconal cystic masses with no extension into the orbital apex or superior orbital fissure (Figure 4). Enlargement of the orbital space however, was seen. In view of these findings, the diagnosis of orbital lymphangioma was considered. Patient underwent excision of the mass as her vision was threatened.


Congenital orbital lymphangioma in a 20-years old girl a case report and review of literature.

Mishra A, Abuhajar R, Alsawidi K, Alaoud M, Ehtuish E - Libyan J Med (2009)

Coronal post-contrast CT scan thin section shows the retrobulbar non-enhancing lesions with preseptal extension.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC3066740&req=5

Figure 0003: Coronal post-contrast CT scan thin section shows the retrobulbar non-enhancing lesions with preseptal extension.
Mentions: A 20-year-old girl presented to the out-patients’ department with unilateral proptosis since birth. This was progressive in nature. There was also an ipsilateral facial deformity with fullness in the supraorbital space (Figure 1). There was no association with pain. There was no history of sudden increase of proptosis. In addition, there was a reduced vision 6/36 in the affected eye. The cornea was clear and so was the lens. Choroidal folds were seen on fundus examination with normal disc and macula. There was no history of redness of the eye. No watery discharge was seen. Ultrasound examination showed multiple cystic intraconal spaces (Figure 2) with very low but turbulent flow. CT scan showed multiple hypodense nonenhancing intraconal lobulated lesions extending into the preseptal space (Figure 3). MRI showed an unencapsulated homogenous lobulated intraconal cystic masses with no extension into the orbital apex or superior orbital fissure (Figure 4). Enlargement of the orbital space however, was seen. In view of these findings, the diagnosis of orbital lymphangioma was considered. Patient underwent excision of the mass as her vision was threatened.

Bottom Line: We report a case of a 20-year-old girl who presented to the out-patients' department with congenital, progressive unilateral proptosis and reduced vision.Diagnosis of orbital lymphangioma was made on imaging.This case is reported because of its extreme rarity and unusual presentation.

View Article: PubMed Central - PubMed

Affiliation: Department of Radiology, National Organ Transplant Centre, Central Hospital, Tripoli, Libya.

ABSTRACT
We report a case of a 20-year-old girl who presented to the out-patients' department with congenital, progressive unilateral proptosis and reduced vision. Ultrasound, computed tomography (CT) scan and magnetic resonance imaging (MRI) were performed. Diagnosis of orbital lymphangioma was made on imaging. Authors highlight the crucial role of imaging in diagnosis and to plan therapeutic approach. This case is reported because of its extreme rarity and unusual presentation.

No MeSH data available.


Related in: MedlinePlus