Limits...
Dermatofibrosarcoma protuberans with fibrosarcomatous transformation of the head and neck.

Angouridakis N, Kafas P, Jerjes W, Triaridis S, Upile T, Karkavelas G, Nikolaou A - Head Neck Oncol (2011)

Bottom Line: Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous neoplasm associated with a high cure rate.A 28-year-old Mediterranean female presented with a 45-day history of rapidly growing cutaneous lesion of the face.Subsequently, the patient underwent wide local surgical resection, followed by reconstruction.

View Article: PubMed Central - HTML - PubMed

Affiliation: Otorhinolaryngology, Head and Neck Surgery Department, AHEPA University Hospital, Thessaloniki, Greece. nikos.angouridakis@gmail.com

ABSTRACT
Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous neoplasm associated with a high cure rate. We present a case of aggressive DFSP with fibrosarcomatous areas in the head and neck. A 28-year-old Mediterranean female presented with a 45-day history of rapidly growing cutaneous lesion of the face. Surgical biopsy confirmed the diagnosis of DFSP. Subsequently, the patient underwent wide local surgical resection, followed by reconstruction. Histopathology report revealed fibrosarcomatous transformation and the patient underwent adjuvant radiotherapy. The patient continues to be disease free at the 35-month follow-up.Although DFSP behave as non-aggressive malignancy, surgery with complete removal of the affected area is the intervention of choice. Moreover, adjuvant treatment and follow-up of the patient is essential in order to prevent recurrence.

Show MeSH

Related in: MedlinePlus

Clinical image showing an infra-auricular lesion (10 × 5 × 4 cm in size).
© Copyright Policy - open-access
Related In: Results  -  Collection

License
getmorefigures.php?uid=PMC3038985&req=5

Figure 1: Clinical image showing an infra-auricular lesion (10 × 5 × 4 cm in size).

Mentions: A 28-year-old Mediterranean female with unremarkable medical history, attended the out-patients department, with a 45-day history of a painless rapidly growing lesion in the right cheek (infra-auricular area). Clinical examination revealed a protruding painless red-bluish mass, which was associated with the skin over the parotid area. The lesion (sized 10 × 5 × 4 cm) was firm, fixed to deeper tissues with propensity to bleed. No facial nerve involvement was noted (Figure 1).


Dermatofibrosarcoma protuberans with fibrosarcomatous transformation of the head and neck.

Angouridakis N, Kafas P, Jerjes W, Triaridis S, Upile T, Karkavelas G, Nikolaou A - Head Neck Oncol (2011)

Clinical image showing an infra-auricular lesion (10 × 5 × 4 cm in size).
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC3038985&req=5

Figure 1: Clinical image showing an infra-auricular lesion (10 × 5 × 4 cm in size).
Mentions: A 28-year-old Mediterranean female with unremarkable medical history, attended the out-patients department, with a 45-day history of a painless rapidly growing lesion in the right cheek (infra-auricular area). Clinical examination revealed a protruding painless red-bluish mass, which was associated with the skin over the parotid area. The lesion (sized 10 × 5 × 4 cm) was firm, fixed to deeper tissues with propensity to bleed. No facial nerve involvement was noted (Figure 1).

Bottom Line: Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous neoplasm associated with a high cure rate.A 28-year-old Mediterranean female presented with a 45-day history of rapidly growing cutaneous lesion of the face.Subsequently, the patient underwent wide local surgical resection, followed by reconstruction.

View Article: PubMed Central - HTML - PubMed

Affiliation: Otorhinolaryngology, Head and Neck Surgery Department, AHEPA University Hospital, Thessaloniki, Greece. nikos.angouridakis@gmail.com

ABSTRACT
Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous neoplasm associated with a high cure rate. We present a case of aggressive DFSP with fibrosarcomatous areas in the head and neck. A 28-year-old Mediterranean female presented with a 45-day history of rapidly growing cutaneous lesion of the face. Surgical biopsy confirmed the diagnosis of DFSP. Subsequently, the patient underwent wide local surgical resection, followed by reconstruction. Histopathology report revealed fibrosarcomatous transformation and the patient underwent adjuvant radiotherapy. The patient continues to be disease free at the 35-month follow-up.Although DFSP behave as non-aggressive malignancy, surgery with complete removal of the affected area is the intervention of choice. Moreover, adjuvant treatment and follow-up of the patient is essential in order to prevent recurrence.

Show MeSH
Related in: MedlinePlus