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Dentin dysplasia type I: a case report and review of the literature.

Toomarian L, Mashhadiabbas F, Mirkarimi M, Mehrdad L - J Med Case Rep (2010)

Bottom Line: There are still many inconclusive issues in the diagnosis and management of patients with dentin dysplasia.The diagnostic features of this rare disturbance will remain incompletely defined until additional cases have been described.Early diagnosis of the condition and initiation of effective regular dental treatments may help these patients to prevent or delay loss of dentition.

View Article: PubMed Central - HTML - PubMed

Affiliation: Pediatric Department, Zahedan University of Medical Sciences, Zahedan, Iran. mirkarimi200@yahoo.com.

ABSTRACT

Introduction: Dentin dysplasia is a rare hereditary disturbance of dentin formation characterized by defective dentin development with clinically normal appearing crowns, severe hypermobility of teeth and spontaneous dental abscesses or cysts. Radiographic analysis shows obliteration of all pulp chambers, short, blunted and malformed or absent roots and peri-apical radiolucencies of non carious teeth.

Case presentation: We present a case of dentin dysplasia type I in a 12-year-old Iranian boy, and the clinical, radiographic and histopathologic findings of this condition and treatment are described.

Conclusions: There are still many inconclusive issues in the diagnosis and management of patients with dentin dysplasia. The diagnostic features of this rare disturbance will remain incompletely defined until additional cases have been described. Early diagnosis of the condition and initiation of effective regular dental treatments may help these patients to prevent or delay loss of dentition.

No MeSH data available.


Related in: MedlinePlus

Panoramic radiography before treatment.
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Figure 4: Panoramic radiography before treatment.

Mentions: The crowns of his teeth had normal morphologic characteristics, but the color of his teeth was slightly more yellow than expected for a patient of his age (Figure 1, Figure 2, Figure 3). Oral hygiene was poor and there were plaque deposits present in all quadrants. The patient's medical history revealed no evidence of disturbance in general health. Caries were present in most of the teeth. The maxillary and mandibular central and lateral incisors were mobile, and there was a painful expansion on the buccal region of the mandibular left first molar. Information supplied by his mother indicated that the child's gingiva had become markedly swollen in both upper and lower jaws on various occasions and that this condition had been treated by antibiotic therapy. Radiographic examination revealed pulpless teeth with no root formation in most teeth and roots of only a few millimeters in some teeth. There was a well-defined round unilocular radiolucency in association with the apex of the left first permanent molar. The left maxillary and mandibular canine teeth were impacted and located horizontally in panoramic view (Figure 4).


Dentin dysplasia type I: a case report and review of the literature.

Toomarian L, Mashhadiabbas F, Mirkarimi M, Mehrdad L - J Med Case Rep (2010)

Panoramic radiography before treatment.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC2823758&req=5

Figure 4: Panoramic radiography before treatment.
Mentions: The crowns of his teeth had normal morphologic characteristics, but the color of his teeth was slightly more yellow than expected for a patient of his age (Figure 1, Figure 2, Figure 3). Oral hygiene was poor and there were plaque deposits present in all quadrants. The patient's medical history revealed no evidence of disturbance in general health. Caries were present in most of the teeth. The maxillary and mandibular central and lateral incisors were mobile, and there was a painful expansion on the buccal region of the mandibular left first molar. Information supplied by his mother indicated that the child's gingiva had become markedly swollen in both upper and lower jaws on various occasions and that this condition had been treated by antibiotic therapy. Radiographic examination revealed pulpless teeth with no root formation in most teeth and roots of only a few millimeters in some teeth. There was a well-defined round unilocular radiolucency in association with the apex of the left first permanent molar. The left maxillary and mandibular canine teeth were impacted and located horizontally in panoramic view (Figure 4).

Bottom Line: There are still many inconclusive issues in the diagnosis and management of patients with dentin dysplasia.The diagnostic features of this rare disturbance will remain incompletely defined until additional cases have been described.Early diagnosis of the condition and initiation of effective regular dental treatments may help these patients to prevent or delay loss of dentition.

View Article: PubMed Central - HTML - PubMed

Affiliation: Pediatric Department, Zahedan University of Medical Sciences, Zahedan, Iran. mirkarimi200@yahoo.com.

ABSTRACT

Introduction: Dentin dysplasia is a rare hereditary disturbance of dentin formation characterized by defective dentin development with clinically normal appearing crowns, severe hypermobility of teeth and spontaneous dental abscesses or cysts. Radiographic analysis shows obliteration of all pulp chambers, short, blunted and malformed or absent roots and peri-apical radiolucencies of non carious teeth.

Case presentation: We present a case of dentin dysplasia type I in a 12-year-old Iranian boy, and the clinical, radiographic and histopathologic findings of this condition and treatment are described.

Conclusions: There are still many inconclusive issues in the diagnosis and management of patients with dentin dysplasia. The diagnostic features of this rare disturbance will remain incompletely defined until additional cases have been described. Early diagnosis of the condition and initiation of effective regular dental treatments may help these patients to prevent or delay loss of dentition.

No MeSH data available.


Related in: MedlinePlus