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Crusted Piloleiomyoma with mental retardation: a rare association.

Kamboj S, Sharma RK, Kumar A, Chaudhary SS, Jain VK - Indian J Dermatol (2009)

Bottom Line: The histopathological features were consistent with Piloleiomyoma.The occurrence of Piloleiomyoma in a mentally retarded child and its unusual crusted nature has been rarely reported.The association between Piloleiomyoma and mental retardation is further stressed in this case report.

View Article: PubMed Central - PubMed

Affiliation: Department of Dermatology, Rajendra Institute of Medical Sciences, Ranchi, India. dermasony@gmail.com

ABSTRACT
Piloleiomyoma is an uncommon benign smooth muscle neoplasm arising from arrector pili muscle. It is clinically defined by the presence of solitary or multiple reddish brown, dome-shaped, smooth papules or nodules, ranging in size from a few millimeters to a centimeter. The patients are otherwise healthy; but mental retardation developing in some patients with multiple Piloleiomyomas has been emerging as an intriguing matter for analysis by the scientists. In this case report, a mentally retarded patient with Piloleiomyoma is described, who, besides the characteristic smooth and dome-shaped lesions on the anterolateral aspect of the dorsum of the right foot, had developed crusting on one of the largest lesions. The histopathological features were consistent with Piloleiomyoma. The occurrence of Piloleiomyoma in a mentally retarded child and its unusual crusted nature has been rarely reported. The association between Piloleiomyoma and mental retardation is further stressed in this case report.

No MeSH data available.


Related in: MedlinePlus

Multiple piloleiomyoma on the dorsum of the foot
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Figure 0001: Multiple piloleiomyoma on the dorsum of the foot

Mentions: A 17-year-old male born of non consanguineous marriage presented with multiple nodules on the dorsum of the right foot, for two years. There was history of spontaneous pain intermittently and also pain on exposure to cold and trauma. The patient was mentally subnormal since childhood, as compared to others of his age. On examination, there was a large swelling of 7cm × 5cm in size, present on the anterolateral aspect of the dorsum of the right foot. Four to five smaller nodules were present adjacent to it. The lesions were well defined, with a smooth surface and firm in consistency. The larger lesion showed central crusting which had occurred, due to spontaneous rupture, two months previously. Swelling was not fixed to the underlying structure [Figure 1]. No other skin or mucus membrane lesion was found. There was no family history of similar lesions. The patient was referred to the department of psychiatry for evaluation of mental intelligence. Applying the WHO criteria, he was diagnosed as having moderate mental retardation. The diagnosis was done after assessment using the Stanford Binet and Bhatia Battery of Intelligence tests, which showed his IQ (Intelligence Quotient) levels to be 38 and 44 respectively. His Magnetic Resonance Imaging (MRI) showed all the structures within normal limits.


Crusted Piloleiomyoma with mental retardation: a rare association.

Kamboj S, Sharma RK, Kumar A, Chaudhary SS, Jain VK - Indian J Dermatol (2009)

Multiple piloleiomyoma on the dorsum of the foot
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC2800880&req=5

Figure 0001: Multiple piloleiomyoma on the dorsum of the foot
Mentions: A 17-year-old male born of non consanguineous marriage presented with multiple nodules on the dorsum of the right foot, for two years. There was history of spontaneous pain intermittently and also pain on exposure to cold and trauma. The patient was mentally subnormal since childhood, as compared to others of his age. On examination, there was a large swelling of 7cm × 5cm in size, present on the anterolateral aspect of the dorsum of the right foot. Four to five smaller nodules were present adjacent to it. The lesions were well defined, with a smooth surface and firm in consistency. The larger lesion showed central crusting which had occurred, due to spontaneous rupture, two months previously. Swelling was not fixed to the underlying structure [Figure 1]. No other skin or mucus membrane lesion was found. There was no family history of similar lesions. The patient was referred to the department of psychiatry for evaluation of mental intelligence. Applying the WHO criteria, he was diagnosed as having moderate mental retardation. The diagnosis was done after assessment using the Stanford Binet and Bhatia Battery of Intelligence tests, which showed his IQ (Intelligence Quotient) levels to be 38 and 44 respectively. His Magnetic Resonance Imaging (MRI) showed all the structures within normal limits.

Bottom Line: The histopathological features were consistent with Piloleiomyoma.The occurrence of Piloleiomyoma in a mentally retarded child and its unusual crusted nature has been rarely reported.The association between Piloleiomyoma and mental retardation is further stressed in this case report.

View Article: PubMed Central - PubMed

Affiliation: Department of Dermatology, Rajendra Institute of Medical Sciences, Ranchi, India. dermasony@gmail.com

ABSTRACT
Piloleiomyoma is an uncommon benign smooth muscle neoplasm arising from arrector pili muscle. It is clinically defined by the presence of solitary or multiple reddish brown, dome-shaped, smooth papules or nodules, ranging in size from a few millimeters to a centimeter. The patients are otherwise healthy; but mental retardation developing in some patients with multiple Piloleiomyomas has been emerging as an intriguing matter for analysis by the scientists. In this case report, a mentally retarded patient with Piloleiomyoma is described, who, besides the characteristic smooth and dome-shaped lesions on the anterolateral aspect of the dorsum of the right foot, had developed crusting on one of the largest lesions. The histopathological features were consistent with Piloleiomyoma. The occurrence of Piloleiomyoma in a mentally retarded child and its unusual crusted nature has been rarely reported. The association between Piloleiomyoma and mental retardation is further stressed in this case report.

No MeSH data available.


Related in: MedlinePlus