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'Rapunzel syndrome' trichobezoar in a 7-year-old girl: a case report.

Al Wadan AH, Al Kaff H, Al Senabani J, Al Saadi AS - Cases J (2008)

Bottom Line: Clinical presentation is deceptive and vague ranging from abdominal mass to gastrointestinal symptoms.We present a 7 years old girl with Rapunzel syndrome, where the trichobezoar was not suspected at all especially with negative history of trichophagia.In the paediatric age group with a long history of gastrointestinal symptom, endoscopy is a diagnostic as well as a therapeutic modality and may reduce surgery in trichobezoars.

View Article: PubMed Central - HTML - PubMed

Affiliation: Kwait University Hospital, Sana'a medical SchooL, Wadi Dhaher Road, P,O, Box 1247, Sana'a, Yemen. azanalsaadi@gmail.com.

ABSTRACT

Background: Rapunzel syndrome is a rare type of trichobezoar with an extension of the hair into the small bowel. Clinical presentation is deceptive and vague ranging from abdominal mass to gastrointestinal symptoms.

Case presentation: We present a 7 years old girl with Rapunzel syndrome, where the trichobezoar was not suspected at all especially with negative history of trichophagia. In majority of the cases the diagnosis was made very late in the history of the disease, at a stage where surgery is the only cure for this syndrome.

Conclusion: In the paediatric age group with a long history of gastrointestinal symptom, endoscopy is a diagnostic as well as a therapeutic modality and may reduce surgery in trichobezoars.

No MeSH data available.


Related in: MedlinePlus

The extension of the hair into the small bowel through entrotomy.
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Figure 2: The extension of the hair into the small bowel through entrotomy.

Mentions: The patient was referred to Surgery, and through upper mid line incision the stomach was opened (Gastrotomy) between two Vicryl stay suture. A huge Trichobezoar was identified which took the shape of the stomach (Figure 1, 2). There was a long tail of hair extending through the pylorus into the small bowel. By this feature the diagnosis was clear of a Rapunzel syndrome. A distal enterotomy was performed (Figure 3) and the remaining part was dislodged gently. Both the opening in the gastric wall and small bowel was closed with continuous Vicryl. The patient had an uneventful postoperative course and was discharged after six days. The parents were advised to visit pediatric psychiatry for follow up.


'Rapunzel syndrome' trichobezoar in a 7-year-old girl: a case report.

Al Wadan AH, Al Kaff H, Al Senabani J, Al Saadi AS - Cases J (2008)

The extension of the hair into the small bowel through entrotomy.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=PMC2567304&req=5

Figure 2: The extension of the hair into the small bowel through entrotomy.
Mentions: The patient was referred to Surgery, and through upper mid line incision the stomach was opened (Gastrotomy) between two Vicryl stay suture. A huge Trichobezoar was identified which took the shape of the stomach (Figure 1, 2). There was a long tail of hair extending through the pylorus into the small bowel. By this feature the diagnosis was clear of a Rapunzel syndrome. A distal enterotomy was performed (Figure 3) and the remaining part was dislodged gently. Both the opening in the gastric wall and small bowel was closed with continuous Vicryl. The patient had an uneventful postoperative course and was discharged after six days. The parents were advised to visit pediatric psychiatry for follow up.

Bottom Line: Clinical presentation is deceptive and vague ranging from abdominal mass to gastrointestinal symptoms.We present a 7 years old girl with Rapunzel syndrome, where the trichobezoar was not suspected at all especially with negative history of trichophagia.In the paediatric age group with a long history of gastrointestinal symptom, endoscopy is a diagnostic as well as a therapeutic modality and may reduce surgery in trichobezoars.

View Article: PubMed Central - HTML - PubMed

Affiliation: Kwait University Hospital, Sana'a medical SchooL, Wadi Dhaher Road, P,O, Box 1247, Sana'a, Yemen. azanalsaadi@gmail.com.

ABSTRACT

Background: Rapunzel syndrome is a rare type of trichobezoar with an extension of the hair into the small bowel. Clinical presentation is deceptive and vague ranging from abdominal mass to gastrointestinal symptoms.

Case presentation: We present a 7 years old girl with Rapunzel syndrome, where the trichobezoar was not suspected at all especially with negative history of trichophagia. In majority of the cases the diagnosis was made very late in the history of the disease, at a stage where surgery is the only cure for this syndrome.

Conclusion: In the paediatric age group with a long history of gastrointestinal symptom, endoscopy is a diagnostic as well as a therapeutic modality and may reduce surgery in trichobezoars.

No MeSH data available.


Related in: MedlinePlus