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Mondini deformity, incomplete partition type I.

Harshany MLH - MedPix

View Article: MedPix Image - MedPix Case

Affiliation: Brooke Army Medical Center

ABSTRACT

Diagnosis: Mondini deformity, incomplete partition type I.

History: 9 year old male with left-sided sensorineural hearing loss.

Findings: High-resolution CT through the petrous bone in axial section shows a cystic cochleovestibular malformation of both ears. The bilateral cochlear turns are incomplete with a small appearance of the apex (last cochlear turn). The bilateral semicircular canals are abnormal with dilatation of the posterior and lateral semicircular canals. The vesibule is dilated on both sides. The vestibular aqueduct appears normal. The findings are bilateral although more pronounced on the right.

Ddx: Mondini Deformity. Large vestibular aqueduct syndrome (can be isolated only to vestibular aqueduct or can be associated with cochlear and vestibular dysplasia) Cochlear hypoplasia (associated with one large cavity between coclea and vestibule) Michel's Aplasia (complete lack of formation. Cock's Deformity). Pendred syndrome.

Dxhow: Radiographically.

Exam: NA.

No MeSH data available.


Left temporal bone - vestibular aqueduct normal but posterior and lateral semicircular canals are dilated.
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MPX2558_synpic20828: Left temporal bone - vestibular aqueduct normal but posterior and lateral semicircular canals are dilated.


Mondini deformity, incomplete partition type I.

Harshany MLH - MedPix

Left temporal bone - vestibular aqueduct normal but posterior and lateral semicircular canals are dilated.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=MPX2558&req=5

MPX2558_synpic20828: Left temporal bone - vestibular aqueduct normal but posterior and lateral semicircular canals are dilated.

View Article: MedPix Image - MedPix Case

Affiliation: Brooke Army Medical Center

ABSTRACT

Diagnosis: Mondini deformity, incomplete partition type I.

History: 9 year old male with left-sided sensorineural hearing loss.

Findings: High-resolution CT through the petrous bone in axial section shows a cystic cochleovestibular malformation of both ears. The bilateral cochlear turns are incomplete with a small appearance of the apex (last cochlear turn). The bilateral semicircular canals are abnormal with dilatation of the posterior and lateral semicircular canals. The vesibule is dilated on both sides. The vestibular aqueduct appears normal. The findings are bilateral although more pronounced on the right.

Ddx: Mondini Deformity. Large vestibular aqueduct syndrome (can be isolated only to vestibular aqueduct or can be associated with cochlear and vestibular dysplasia) Cochlear hypoplasia (associated with one large cavity between coclea and vestibule) Michel's Aplasia (complete lack of formation. Cock's Deformity). Pendred syndrome.

Dxhow: Radiographically.

Exam: NA.

No MeSH data available.