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Poland Syndrome

Barnes MGB - MedPix (2007)

View Article: MedPix Image - MedPix Case

Affiliation: Uniformed Services University

ABSTRACT

Diagnosis: Poland Syndrome

History: 1 day old male is presenting for radiological evaluation of apparent hand deformity (noticed by the mother).

Findings: A plain film portable view of the lungs demonstrate that they are well expanded and clear. The cardiothymic silhouette and pulmonary vascularity are within normal limits. The right lung is more lucent than the left, with absence of the pectoralis shadow. A portable plain film view of the right hand was performed and demonstrates deformity of the 2nd and 3rd phalanges. The metacarpals are all present and normal. The proximal phalanges of all digits are present. The distal phalanges of all digits appear present. However, the middle phalanges of all digits are not visualized. There is radial deviation of all digits of the metacarpophalangeal joints with ulnar deviation of the distal thumb, index finger and middle finger. There is significant overlap of soft tissues especially on the radial side and evaluation of soft tissues is limited. Fusion of the soft tissues may be present.

Ddx: Poland Syndrome CHILD Syndrome Thoracic Hemivertebrae

Dxhow: Genetic Counseling

Exam: VS: 98 degrees, P: 128, RR: 44. Weight: 3462g. Gen: No Acute Distress. HEENT: NC/AT. Flat Affect. CV: RRR. No murmurs. Pulm: CTAB, No signs of respiratory distress. Chest: Right Chest Assymetry (less size than left chest), Right Nipple looks smaller than Left Nipple. Abd: NABS, NT, NG, ND, No HSM, No Masses. Derm: No Jaundice. Extremity: Full ROM, Barlow/Ortolani negative, Right Hand is hypoplastic with absence of 2nd and 3rd phalanx, and Right Arm seems smaller than the left arm.

No MeSH data available.


A portable plain film view of the right hand was performed and demonstrates deformity of the 2nd and 3rd phalanges.  The metacarpals are all present and normal.  The proximal phalanges of all digits are present.  The distal phalanges of all digits appear present.  However, the middle phalanges of all digits are not visualized.  There is radial deviation of all digits of the metacarpophalangeal joints with ulnar deviation of the distal thumb, index finger and middle finger.  There is significant overlap of soft tissues especially on the radial side and evaluation of soft tissues is limited.  Fusion of the soft tissues may be present.
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MPX2311_synpic38651: A portable plain film view of the right hand was performed and demonstrates deformity of the 2nd and 3rd phalanges. The metacarpals are all present and normal. The proximal phalanges of all digits are present. The distal phalanges of all digits appear present. However, the middle phalanges of all digits are not visualized. There is radial deviation of all digits of the metacarpophalangeal joints with ulnar deviation of the distal thumb, index finger and middle finger. There is significant overlap of soft tissues especially on the radial side and evaluation of soft tissues is limited. Fusion of the soft tissues may be present.


Poland Syndrome

Barnes MGB - MedPix (2007)

A portable plain film view of the right hand was performed and demonstrates deformity of the 2nd and 3rd phalanges.  The metacarpals are all present and normal.  The proximal phalanges of all digits are present.  The distal phalanges of all digits appear present.  However, the middle phalanges of all digits are not visualized.  There is radial deviation of all digits of the metacarpophalangeal joints with ulnar deviation of the distal thumb, index finger and middle finger.  There is significant overlap of soft tissues especially on the radial side and evaluation of soft tissues is limited.  Fusion of the soft tissues may be present.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=MPX2311&req=5

MPX2311_synpic38651: A portable plain film view of the right hand was performed and demonstrates deformity of the 2nd and 3rd phalanges. The metacarpals are all present and normal. The proximal phalanges of all digits are present. The distal phalanges of all digits appear present. However, the middle phalanges of all digits are not visualized. There is radial deviation of all digits of the metacarpophalangeal joints with ulnar deviation of the distal thumb, index finger and middle finger. There is significant overlap of soft tissues especially on the radial side and evaluation of soft tissues is limited. Fusion of the soft tissues may be present.

View Article: MedPix Image - MedPix Case

Affiliation: Uniformed Services University

ABSTRACT

Diagnosis: Poland Syndrome

History: 1 day old male is presenting for radiological evaluation of apparent hand deformity (noticed by the mother).

Findings: A plain film portable view of the lungs demonstrate that they are well expanded and clear. The cardiothymic silhouette and pulmonary vascularity are within normal limits. The right lung is more lucent than the left, with absence of the pectoralis shadow. A portable plain film view of the right hand was performed and demonstrates deformity of the 2nd and 3rd phalanges. The metacarpals are all present and normal. The proximal phalanges of all digits are present. The distal phalanges of all digits appear present. However, the middle phalanges of all digits are not visualized. There is radial deviation of all digits of the metacarpophalangeal joints with ulnar deviation of the distal thumb, index finger and middle finger. There is significant overlap of soft tissues especially on the radial side and evaluation of soft tissues is limited. Fusion of the soft tissues may be present.

Ddx: Poland Syndrome CHILD Syndrome Thoracic Hemivertebrae

Dxhow: Genetic Counseling

Exam: VS: 98 degrees, P: 128, RR: 44. Weight: 3462g. Gen: No Acute Distress. HEENT: NC/AT. Flat Affect. CV: RRR. No murmurs. Pulm: CTAB, No signs of respiratory distress. Chest: Right Chest Assymetry (less size than left chest), Right Nipple looks smaller than Left Nipple. Abd: NABS, NT, NG, ND, No HSM, No Masses. Derm: No Jaundice. Extremity: Full ROM, Barlow/Ortolani negative, Right Hand is hypoplastic with absence of 2nd and 3rd phalanx, and Right Arm seems smaller than the left arm.

No MeSH data available.