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VACTERL Syndrome

Gilman LAG - MedPix (2009)

View Article: MedPix Image - MedPix Case

Affiliation: Naval Medical Center San Diego

ABSTRACT

Diagnosis: VACTERL Syndrome

History: 56 d/o male in NICU with history of imperforate anus, malrotation, tracheal and esophageal atresia, s/p multiple bowel surgeries and gastrostomy tube placement who presents with decreased lung sounds throughout the R lung and collapsed RMSB on bronchoscopy.

Findings: CXR DOL 0: Endotracheal tube with distal tip over the top of the carina. Enteric tube with the distal tip lying over the clavicular heads in the setting of known esophageal atresia. CT CHEST W/ & W/O CONTRAST DOL 56: 1. R-SIDED AORTA W/ RMSB INTERPOSED BETWEEN THE DESCENDING AORTA AND R PULM ARTERY RESULTING IN CONSOLIDATION AND ATELECTASIS IN R LUNG BASE. 2. DISTAL TRACHEAL ATRESIA AND BRONCHIAL ATRESIA. 3. ESOPHAGEAL ATRESIA W/ BLIND ENDING POUCH ENDING JUST ABOVE THE AORTIC ARCH. 4. LIVER IS ENLARGED W/ LIKELY 2CM ABSCESS IN R HEPATIC LOBE. SPLEEN ENLARGED MEASURING 7.4 CM CRANIOCAUDALLY. 5. MIDLINE FUSION OF INFERIOR POLES SUGGESTIVE OF HORSESHOE KIDNEY.

Ddx: • PHAVER Syndrome • Patau Syndrome (T13) • Edward's Syndrome (T18) • Tracheoesophageal Fistula • VACTERL Syndrome

Dxhow: Clinical Examination, Multiple Congenital Abnormalities (5 categories) on CT CHEST

Exam: CVS/Resp: Decreased lung sounds throughout R lung fields, most notable in the base. RRR, NS1S2. Abd: Gastrostomy tube visible, site clean. Bowel sounds present throughout. Anal surgery site clean.

No MeSH data available.


The spleen is markedly enlarged, measuring 7.4 cm in a craniocaudal extent.
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MPX2102_synpic51462: The spleen is markedly enlarged, measuring 7.4 cm in a craniocaudal extent.


VACTERL Syndrome

Gilman LAG - MedPix (2009)

The spleen is markedly enlarged, measuring 7.4 cm in a craniocaudal extent.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=MPX2102&req=5

MPX2102_synpic51462: The spleen is markedly enlarged, measuring 7.4 cm in a craniocaudal extent.

View Article: MedPix Image - MedPix Case

Affiliation: Naval Medical Center San Diego

ABSTRACT

Diagnosis: VACTERL Syndrome

History: 56 d/o male in NICU with history of imperforate anus, malrotation, tracheal and esophageal atresia, s/p multiple bowel surgeries and gastrostomy tube placement who presents with decreased lung sounds throughout the R lung and collapsed RMSB on bronchoscopy.

Findings: CXR DOL 0: Endotracheal tube with distal tip over the top of the carina. Enteric tube with the distal tip lying over the clavicular heads in the setting of known esophageal atresia. CT CHEST W/ & W/O CONTRAST DOL 56: 1. R-SIDED AORTA W/ RMSB INTERPOSED BETWEEN THE DESCENDING AORTA AND R PULM ARTERY RESULTING IN CONSOLIDATION AND ATELECTASIS IN R LUNG BASE. 2. DISTAL TRACHEAL ATRESIA AND BRONCHIAL ATRESIA. 3. ESOPHAGEAL ATRESIA W/ BLIND ENDING POUCH ENDING JUST ABOVE THE AORTIC ARCH. 4. LIVER IS ENLARGED W/ LIKELY 2CM ABSCESS IN R HEPATIC LOBE. SPLEEN ENLARGED MEASURING 7.4 CM CRANIOCAUDALLY. 5. MIDLINE FUSION OF INFERIOR POLES SUGGESTIVE OF HORSESHOE KIDNEY.

Ddx: • PHAVER Syndrome • Patau Syndrome (T13) • Edward's Syndrome (T18) • Tracheoesophageal Fistula • VACTERL Syndrome

Dxhow: Clinical Examination, Multiple Congenital Abnormalities (5 categories) on CT CHEST

Exam: CVS/Resp: Decreased lung sounds throughout R lung fields, most notable in the base. RRR, NS1S2. Abd: Gastrostomy tube visible, site clean. Bowel sounds present throughout. Anal surgery site clean.

No MeSH data available.