Limits...
Pulmonary manifestations of Neurofibromatosis 1. However, pulmonary fibrosis with bullous formation from smoking related pulmonary diseases can’t be ruled out.

Wilson AMW - MedPix

View Article: MedPix Image - MedPix Case

Affiliation: Madigan Army Medical Center

ABSTRACT

Diagnosis: Pulmonary manifestations of Neurofibromatosis 1. However, pulmonary fibrosis with bullous formation from smoking related pulmonary diseases can’t be ruled out.

History: 66 y.o. female with NF1, vomiting, 25 pack year smoking history, No history of COPD. CXR obtained initially and Chest CT later obtained for further evaluation of CXR findings.

Findings: CXR: Ill-defined density in upper lateral peri-hilar region on PA view, not definitively seen on lateral projection, but possibly more anterior. CT, chest w/contrast: Multiple soft tissue attenuated skin nodules noted on anterior chest. No pulmonary nodules or masses seen. Pulmonary fibrosis with honey-combing predominately occurring in the upper lobes. Bullous changes are seen adjacent to mediastinum near azygoesophageal recess. Pulmonary scaring and honey-combing extends to right lower lung.

Ddx: Emphysema Idiopathic Pulmonary Fibrosis (IPF) Autoimmune disorders (Sarcoidosis, RA) Collagen-vascular diseases with fibrosising aveolitits

Exam: not available

No MeSH data available.


Multiple soft tissue attenuated skin nodules noted on anterior chest. No pulmonary nodules or masses seen.  Pulmonary fibrosis with honey-combing predominately occurring in the upper lobes. Bullous changes are seen adjacent to mediastinum near azygoesophageal recess. Pulmonary scaring and honey-combing extends to right lower lung.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
getmorefigures.php?uid=MPX2016&req=5

MPX2016_synpic24560: Multiple soft tissue attenuated skin nodules noted on anterior chest. No pulmonary nodules or masses seen. Pulmonary fibrosis with honey-combing predominately occurring in the upper lobes. Bullous changes are seen adjacent to mediastinum near azygoesophageal recess. Pulmonary scaring and honey-combing extends to right lower lung.


Pulmonary manifestations of Neurofibromatosis 1. However, pulmonary fibrosis with bullous formation from smoking related pulmonary diseases can’t be ruled out.

Wilson AMW - MedPix

Multiple soft tissue attenuated skin nodules noted on anterior chest. No pulmonary nodules or masses seen.  Pulmonary fibrosis with honey-combing predominately occurring in the upper lobes. Bullous changes are seen adjacent to mediastinum near azygoesophageal recess. Pulmonary scaring and honey-combing extends to right lower lung.
© Copyright Policy - open-access
Related In: Results  -  Collection

License
Show All Figures
getmorefigures.php?uid=MPX2016&req=5

MPX2016_synpic24560: Multiple soft tissue attenuated skin nodules noted on anterior chest. No pulmonary nodules or masses seen. Pulmonary fibrosis with honey-combing predominately occurring in the upper lobes. Bullous changes are seen adjacent to mediastinum near azygoesophageal recess. Pulmonary scaring and honey-combing extends to right lower lung.

View Article: MedPix Image - MedPix Case

Affiliation: Madigan Army Medical Center

ABSTRACT

Diagnosis: Pulmonary manifestations of Neurofibromatosis 1. However, pulmonary fibrosis with bullous formation from smoking related pulmonary diseases can’t be ruled out.

History: 66 y.o. female with NF1, vomiting, 25 pack year smoking history, No history of COPD. CXR obtained initially and Chest CT later obtained for further evaluation of CXR findings.

Findings: CXR: Ill-defined density in upper lateral peri-hilar region on PA view, not definitively seen on lateral projection, but possibly more anterior. CT, chest w/contrast: Multiple soft tissue attenuated skin nodules noted on anterior chest. No pulmonary nodules or masses seen. Pulmonary fibrosis with honey-combing predominately occurring in the upper lobes. Bullous changes are seen adjacent to mediastinum near azygoesophageal recess. Pulmonary scaring and honey-combing extends to right lower lung.

Ddx: Emphysema Idiopathic Pulmonary Fibrosis (IPF) Autoimmune disorders (Sarcoidosis, RA) Collagen-vascular diseases with fibrosising aveolitits

Exam: not available

No MeSH data available.